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Interrupted Aortic Arch in an Adult with Polycystic Kidney Disease

Autosomal dominant polycystic kidney disease (ADPKD) is the most common hereditary kidney disease and is responsible for 8–10% of patients with end-stage renal failure. The major extrarenal complications of ADPKD are cardiovascular abnormalities. Interrupted aortic arch (IAA) is a lethal congenital...

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Autores principales: Şeker Koçkara, Ayşe, Kayataş, Mansur, Huzmeli, Can, Candan, Ferhan, Gümüş, Cesur
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi Publishing Corporation 2013
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3690743/
https://www.ncbi.nlm.nih.gov/pubmed/23840219
http://dx.doi.org/10.1155/2013/404710
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author Şeker Koçkara, Ayşe
Kayataş, Mansur
Huzmeli, Can
Candan, Ferhan
Gümüş, Cesur
author_facet Şeker Koçkara, Ayşe
Kayataş, Mansur
Huzmeli, Can
Candan, Ferhan
Gümüş, Cesur
author_sort Şeker Koçkara, Ayşe
collection PubMed
description Autosomal dominant polycystic kidney disease (ADPKD) is the most common hereditary kidney disease and is responsible for 8–10% of patients with end-stage renal failure. The major extrarenal complications of ADPKD are cardiovascular abnormalities. Interrupted aortic arch (IAA) is a lethal congenital cardiac abnormality seen with a frequency of 3/1000000 births and is defined as a segment of the arcus aorta being atresic. In the literature, there are no any reports showing that polycystic kidney disease and interrupted aortic arch occur together. In this study, we present a rare case in which the patient has polycystic kidney disease and IAA together and discuss whether IAA is a complication of ADPKD.
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spelling pubmed-36907432013-07-09 Interrupted Aortic Arch in an Adult with Polycystic Kidney Disease Şeker Koçkara, Ayşe Kayataş, Mansur Huzmeli, Can Candan, Ferhan Gümüş, Cesur Case Rep Med Case Report Autosomal dominant polycystic kidney disease (ADPKD) is the most common hereditary kidney disease and is responsible for 8–10% of patients with end-stage renal failure. The major extrarenal complications of ADPKD are cardiovascular abnormalities. Interrupted aortic arch (IAA) is a lethal congenital cardiac abnormality seen with a frequency of 3/1000000 births and is defined as a segment of the arcus aorta being atresic. In the literature, there are no any reports showing that polycystic kidney disease and interrupted aortic arch occur together. In this study, we present a rare case in which the patient has polycystic kidney disease and IAA together and discuss whether IAA is a complication of ADPKD. Hindawi Publishing Corporation 2013 2013-06-09 /pmc/articles/PMC3690743/ /pubmed/23840219 http://dx.doi.org/10.1155/2013/404710 Text en Copyright © 2013 Ayşe Şeker Koçkara et al. https://creativecommons.org/licenses/by/3.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Şeker Koçkara, Ayşe
Kayataş, Mansur
Huzmeli, Can
Candan, Ferhan
Gümüş, Cesur
Interrupted Aortic Arch in an Adult with Polycystic Kidney Disease
title Interrupted Aortic Arch in an Adult with Polycystic Kidney Disease
title_full Interrupted Aortic Arch in an Adult with Polycystic Kidney Disease
title_fullStr Interrupted Aortic Arch in an Adult with Polycystic Kidney Disease
title_full_unstemmed Interrupted Aortic Arch in an Adult with Polycystic Kidney Disease
title_short Interrupted Aortic Arch in an Adult with Polycystic Kidney Disease
title_sort interrupted aortic arch in an adult with polycystic kidney disease
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3690743/
https://www.ncbi.nlm.nih.gov/pubmed/23840219
http://dx.doi.org/10.1155/2013/404710
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