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A Rapid and Sensitive Method for Measuring N-Acetylglucosaminidase Activity in Cultured Cells
A rapid and sensitive method to quantitatively assess N-acetylglucosaminidase (NAG) activity in cultured cells is highly desirable for both basic research and clinical studies. NAG activity is deficient in cells from patients with Mucopolysaccharidosis type IIIB (MPS IIIB) due to mutations in NAGLU,...
Autores principales: | Mauri, Victor, Lotfi, Parisa, Segatori, Laura, Sardiello, Marco |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Public Library of Science
2013
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3695942/ https://www.ncbi.nlm.nih.gov/pubmed/23840811 http://dx.doi.org/10.1371/journal.pone.0068060 |
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