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Uncommon of the Uncommon: Malignant Perivascular Epithelioid Cell Tumor of the Lung

A perivascular epithelioid cell (PEC) tumor is a rare mesenchymal tumor characterized by abundant cytoplasmic Periodic acid-Schiff positive glycogen (also called sugar tumor or clear cell tumor of the lung for this characteristic) and is mostly benign. We report a case of a 63-year-old man who prese...

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Autores principales: Lim, Hyun-ju, Lee, Ho Yun, Han, Joungho, Choi, Yong Soo, Lee, Kyung Soo
Formato: Online Artículo Texto
Lenguaje:English
Publicado: The Korean Society of Radiology 2013
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3725366/
https://www.ncbi.nlm.nih.gov/pubmed/23901329
http://dx.doi.org/10.3348/kjr.2013.14.4.692
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author Lim, Hyun-ju
Lee, Ho Yun
Han, Joungho
Choi, Yong Soo
Lee, Kyung Soo
author_facet Lim, Hyun-ju
Lee, Ho Yun
Han, Joungho
Choi, Yong Soo
Lee, Kyung Soo
author_sort Lim, Hyun-ju
collection PubMed
description A perivascular epithelioid cell (PEC) tumor is a rare mesenchymal tumor characterized by abundant cytoplasmic Periodic acid-Schiff positive glycogen (also called sugar tumor or clear cell tumor of the lung for this characteristic) and is mostly benign. We report a case of a 63-year-old man who presented with an enlarging mass on chest radiograph. After a thorough workup, diagnosis of malignant pulmonary PEC tumor with lung to lung metastases was established. Herein, the difficulties of diagnosis and management we confronted are described.
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spelling pubmed-37253662013-07-30 Uncommon of the Uncommon: Malignant Perivascular Epithelioid Cell Tumor of the Lung Lim, Hyun-ju Lee, Ho Yun Han, Joungho Choi, Yong Soo Lee, Kyung Soo Korean J Radiol Thoracic Imaging A perivascular epithelioid cell (PEC) tumor is a rare mesenchymal tumor characterized by abundant cytoplasmic Periodic acid-Schiff positive glycogen (also called sugar tumor or clear cell tumor of the lung for this characteristic) and is mostly benign. We report a case of a 63-year-old man who presented with an enlarging mass on chest radiograph. After a thorough workup, diagnosis of malignant pulmonary PEC tumor with lung to lung metastases was established. Herein, the difficulties of diagnosis and management we confronted are described. The Korean Society of Radiology 2013 2013-07-17 /pmc/articles/PMC3725366/ /pubmed/23901329 http://dx.doi.org/10.3348/kjr.2013.14.4.692 Text en Copyright © 2013 The Korean Society of Radiology http://creativecommons.org/licenses/by-nc/3.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Thoracic Imaging
Lim, Hyun-ju
Lee, Ho Yun
Han, Joungho
Choi, Yong Soo
Lee, Kyung Soo
Uncommon of the Uncommon: Malignant Perivascular Epithelioid Cell Tumor of the Lung
title Uncommon of the Uncommon: Malignant Perivascular Epithelioid Cell Tumor of the Lung
title_full Uncommon of the Uncommon: Malignant Perivascular Epithelioid Cell Tumor of the Lung
title_fullStr Uncommon of the Uncommon: Malignant Perivascular Epithelioid Cell Tumor of the Lung
title_full_unstemmed Uncommon of the Uncommon: Malignant Perivascular Epithelioid Cell Tumor of the Lung
title_short Uncommon of the Uncommon: Malignant Perivascular Epithelioid Cell Tumor of the Lung
title_sort uncommon of the uncommon: malignant perivascular epithelioid cell tumor of the lung
topic Thoracic Imaging
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3725366/
https://www.ncbi.nlm.nih.gov/pubmed/23901329
http://dx.doi.org/10.3348/kjr.2013.14.4.692
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