Cargando…

Revertant Fibers in the mdx Murine Model of Duchenne Muscular Dystrophy: An Age- and Muscle-Related Reappraisal

Muscles in Duchenne dystrophy patients are characterized by the absence of dystrophin, yet transverse sections show a small percentage of fibers (termed “revertant fibers”) positive for dystrophin expression. This phenomenon, whose biological bases have not been fully elucidated, is present also in...

Descripción completa

Detalles Bibliográficos
Autores principales:	Pigozzo, Sarah R., Da Re, Lorena, Romualdi, Chiara, Mazzara, Pietro G., Galletta, Eva, Fletcher, Sue, Wilton, Stephen D., Vitiello, Libero
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Public Library of Science 2013
Materias:	Research Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3756063/ https://www.ncbi.nlm.nih.gov/pubmed/24015212 http://dx.doi.org/10.1371/journal.pone.0072147

Ejemplares similares

Social stress is lethal in the mdx model of Duchenne muscular dystrophy
por: Razzoli, Maria, et al.
Publicado: (2020)

Novel compounds for the treatment of Duchenne muscular dystrophy: emerging therapeutic agents
por: Wilton, Steve D, et al.
Publicado: (2011)

Biomarkers for Duchenne muscular dystrophy progression: impact of age in the mdx tongue spared muscle
por: Lorena, Marcelo dos Santos Voltani, et al.
Publicado: (2023)

Biomarkers for Duchenne muscular dystrophy progression: impact of age in the mdx tongue spared muscle
por: Lorena, Marcelo dos Santos Voltani, et al.
Publicado: (2023)

Teaching an Old Molecule New Tricks: Drug Repositioning for Duchenne Muscular Dystrophy
por: Vitiello, Libero, et al.
Publicado: (2019)

Drug Repurposing for Duchenne Muscular Dystrophy: The Monoamine Oxidase B Inhibitor Safinamide Ameliorates the Pathological Phenotype in mdx Mice and in Myogenic Cultures From DMD Patients
por: Vitiello, Libero, et al.
Publicado: (2018)

Induction of revertant fibres in the mdx mouse using antisense oligonucleotides
por: Fall, Abbie M, et al.
Publicado: (2006)

Skeletal Muscle Fibrosis in the mdx/utrn+/- Mouse Validates Its Suitability as a Murine Model of Duchenne Muscular Dystrophy
por: Gutpell, Kelly M., et al.
Publicado: (2015)

Ventilatory Chemosensory Drive Is Blunted in the mdx Mouse Model of Duchenne Muscular Dystrophy (DMD)
por: Mosqueira, Matias, et al.
Publicado: (2013)

Naproxcinod shows significant advantages over naproxen in the mdx model of Duchenne Muscular Dystrophy
por: Miglietta, Daniela, et al.
Publicado: (2015)

Comparison of Experimental Protocols of Physical Exercise for mdx Mice and Duchenne Muscular Dystrophy Patients
por: Hyzewicz, Janek, et al.
Publicado: (2015)

Natural disease history of the D2-mdx mouse model for Duchenne muscular dystrophy
por: van Putten, Maaike, et al.
Publicado: (2019)

In vivo cerebellar circuit function is disrupted in an mdx mouse model of Duchenne muscular dystrophy
por: Stay, Trace L., et al.
Publicado: (2019)

Emotional behavior and brain anatomy of the mdx52 mouse model of Duchenne muscular dystrophy
por: Saoudi, Amel, et al.
Publicado: (2021)

miR-378 affects metabolic disturbances in the mdx model of Duchenne muscular dystrophy
por: Podkalicka, Paulina, et al.
Publicado: (2022)

A Novel Method for Detecting Duchenne Muscular Dystrophy in Blood Serum of mdx Mice
por: Ralbovsky, Nicole M., et al.
Publicado: (2022)

Humanization of the mdx Mouse Phenotype for Duchenne Muscular Dystrophy Modeling: A Metabolic Perspective
por: Donen, Graham, et al.
Publicado: (2023)

Dystropathology Increases Energy Expenditure and Protein Turnover in the Mdx Mouse Model of Duchenne Muscular Dystrophy
por: Radley-Crabb, Hannah G., et al.
Publicado: (2014)

Disease course in mdx:utrophin(+/−) mice: comparison of three mouse models of Duchenne muscular dystrophy
por: McDonald, Abby A, et al.
Publicado: (2015)

The Effect of Vitamin D Supplementation on Skeletal Muscle in the mdx Mouse Model of Duchenne Muscular Dystrophy
por: Debruin, Danielle A., et al.
Publicado: (2019)

Myelination is delayed during postnatal brain development in the mdx mouse model of Duchenne muscular dystrophy
por: Aranmolate, Azeez, et al.
Publicado: (2017)

Cardiovascular phenotype of the Dmd(mdx) rat – a suitable animal model for Duchenne muscular dystrophy
por: Szabó, Petra Lujza, et al.
Publicado: (2021)

Lipocalin 2 Influences Bone and Muscle Phenotype in the MDX Mouse Model of Duchenne Muscular Dystrophy
por: Ponzetti, Marco, et al.
Publicado: (2022)

Growth hormone secretagogues modulate inflammation and fibrosis in mdx mouse model of Duchenne muscular dystrophy
por: Boccanegra, Brigida, et al.
Publicado: (2023)

RANKL Inhibition Reduces Cardiac Hypertrophy in mdx Mice and Possibly in Children with Duchenne Muscular Dystrophy
por: Marcadet, Laetitia, et al.
Publicado: (2023)

Recent Trends in Antisense Therapies for Duchenne Muscular Dystrophy
por: Wilton-Clark, Harry, et al.
Publicado: (2023)

Applications of metabolomics and proteomics to the mdx mouse model of Duchenne muscular dystrophy: lessons from downstream of the transcriptome
por: Griffin, Julian L, et al.
Publicado: (2009)

Differential effects of PDE5 inhibitors on cardiac dysfunction in the MDX ouse model of Duchenne muscular dystrophy
por: Rybalkin, Sergei D, et al.
Publicado: (2013)

Altered social behavior and ultrasonic communication in the dystrophin-deficient mdx mouse model of Duchenne muscular dystrophy
por: Miranda, Rubén, et al.
Publicado: (2015)

Whole-body clearing, staining and screening of calcium deposits in the mdx mouse model of Duchenne muscular dystrophy
por: Bozycki, Lukasz, et al.
Publicado: (2018)

Increased plasma lipid levels exacerbate muscle pathology in the mdx mouse model of Duchenne muscular dystrophy
por: Milad, Nadia, et al.
Publicado: (2017)

Proteomic profiling of liver tissue from the mdx-4cv mouse model of Duchenne muscular dystrophy
por: Murphy, Sandra, et al.
Publicado: (2018)

Diagnosis of a model of Duchenne muscular dystrophy in blood serum of mdx mice using Raman hyperspectroscopy
por: Ralbovsky, Nicole M., et al.
Publicado: (2020)

Assessment of Behavioral Characteristics With Procedures of Minimal Human Interference in the mdx Mouse Model for Duchenne Muscular Dystrophy
por: Engelbeen, Sarah, et al.
Publicado: (2021)

Ultrasonography validation for early alteration of diaphragm echodensity and function in the mdx mouse model of Duchenne muscular dystrophy
por: Mele, Antonietta, et al.
Publicado: (2021)

Inhibition of muscle fibrosis results in increases in both utrophin levels and the number of revertant myofibers in Duchenne muscular dystrophy
por: Levi, Oshrat, et al.
Publicado: (2015)

Sphingosine Phosphate Lyase Is Upregulated in Duchenne Muscular Dystrophy, and Its Inhibition Early in Life Attenuates Inflammation and Dystrophy in Mdx Mice
por: De la Garza-Rodea, Anabel S., et al.
Publicado: (2022)

Current Translational Research and Murine Models For Duchenne Muscular Dystrophy
por: Rodrigues, Merryl, et al.
Publicado: (2016)

Adenylosuccinic acid therapy ameliorates murine Duchenne Muscular Dystrophy
por: Timpani, Cara A., et al.
Publicado: (2020)

Functional and Molecular Effects of Arginine Butyrate and Prednisone on Muscle and Heart in the mdx Mouse Model of Duchenne Muscular Dystrophy
por: Guerron, Alfredo D., et al.
Publicado: (2010)

Cannot write session to /tmp/vufind_sessions/sess_6fpr1ejbrgptarqsutfmh7moci