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A case of recurrent pericardial constriction presenting with severe pulmonary hypertension

Chronic constrictive pericarditis (CP) is a relatively rare condition in which the pericardium becomes fibrotic and noncompliant, eventually resulting in heart failure due to impaired ventricular filling. The only curative treatment is pericardiectomy. Classically, CP does not usually cause severe p...

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Detalles Bibliográficos
Autores principales: Brunner, Nathan W., Ramachandran, Krithika, Kudelko, Kristina T., Sung, Yon K., Spiekerkoetter, Edda, Yang, Phillip C., Zamanian, Roham T., Perez, Vinicio de Jesus
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2013
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3757841/
https://www.ncbi.nlm.nih.gov/pubmed/24015347
http://dx.doi.org/10.4103/2045-8932.114780
Descripción
Sumario:Chronic constrictive pericarditis (CP) is a relatively rare condition in which the pericardium becomes fibrotic and noncompliant, eventually resulting in heart failure due to impaired ventricular filling. The only curative treatment is pericardiectomy. Classically, CP does not usually cause severe pulmonary hypertension. When attempting to differentiate CP from restrictive cardiomyopathy, the presence of severely elevated pulmonary arterial pressure is used as a diagnostic criterion ruling against CP. We present a case of proven recurrent pericardial constriction following pericardiectomy presenting with severe pulmonary hypertension.