Pulmonary arterial hypertension combined with a high cardiac output state: Three remarkable cases

A congenital extrahepatic portosystemic venous shunt (CEPVS), also known as an Abernethy malformation, is a rare cause of pulmonary arterial hypertension (PAH). In this case series, we describe three male patients of 30, 23, and 27 years of age with PAH due to a CEPVS. In all three patients, a right...

Descripción completa

Detalles Bibliográficos
Autores principales: Spruijt, Onno A., Bogaard, Harm-Jan, Vonk-Noordegraaf, Anton
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2013
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3757842/
https://www.ncbi.nlm.nih.gov/pubmed/24015348
http://dx.doi.org/10.4103/2045-8932.113185
_version_ 1782282281213231104
author Spruijt, Onno A.
Bogaard, Harm-Jan
Vonk-Noordegraaf, Anton
author_facet Spruijt, Onno A.
Bogaard, Harm-Jan
Vonk-Noordegraaf, Anton
author_sort Spruijt, Onno A.
collection PubMed
description A congenital extrahepatic portosystemic venous shunt (CEPVS), also known as an Abernethy malformation, is a rare cause of pulmonary arterial hypertension (PAH). In this case series, we describe three male patients of 30, 23, and 27 years of age with PAH due to a CEPVS. In all three patients, a right heart catheterization revealed a high cardiac output. The aim of this case series is to make pulmonary hypertension physicians aware of the possibility of a CEPVS when PAH is accompanied with a high cardiac output state.
format Online
Article
Text
id pubmed-3757842
institution National Center for Biotechnology Information
language English
publishDate 2013
publisher Medknow Publications & Media Pvt Ltd
record_format MEDLINE/PubMed
spelling pubmed-37578422013-09-06 Pulmonary arterial hypertension combined with a high cardiac output state: Three remarkable cases Spruijt, Onno A. Bogaard, Harm-Jan Vonk-Noordegraaf, Anton Pulm Circ Case Report A congenital extrahepatic portosystemic venous shunt (CEPVS), also known as an Abernethy malformation, is a rare cause of pulmonary arterial hypertension (PAH). In this case series, we describe three male patients of 30, 23, and 27 years of age with PAH due to a CEPVS. In all three patients, a right heart catheterization revealed a high cardiac output. The aim of this case series is to make pulmonary hypertension physicians aware of the possibility of a CEPVS when PAH is accompanied with a high cardiac output state. Medknow Publications & Media Pvt Ltd 2013 /pmc/articles/PMC3757842/ /pubmed/24015348 http://dx.doi.org/10.4103/2045-8932.113185 Text en Copyright: © Pulmonary Circulation http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Spruijt, Onno A.
Bogaard, Harm-Jan
Vonk-Noordegraaf, Anton
Pulmonary arterial hypertension combined with a high cardiac output state: Three remarkable cases
title Pulmonary arterial hypertension combined with a high cardiac output state: Three remarkable cases
title_full Pulmonary arterial hypertension combined with a high cardiac output state: Three remarkable cases
title_fullStr Pulmonary arterial hypertension combined with a high cardiac output state: Three remarkable cases
title_full_unstemmed Pulmonary arterial hypertension combined with a high cardiac output state: Three remarkable cases
title_short Pulmonary arterial hypertension combined with a high cardiac output state: Three remarkable cases
title_sort pulmonary arterial hypertension combined with a high cardiac output state: three remarkable cases
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3757842/
https://www.ncbi.nlm.nih.gov/pubmed/24015348
http://dx.doi.org/10.4103/2045-8932.113185
work_keys_str_mv AT spruijtonnoa pulmonaryarterialhypertensioncombinedwithahighcardiacoutputstatethreeremarkablecases
AT bogaardharmjan pulmonaryarterialhypertensioncombinedwithahighcardiacoutputstatethreeremarkablecases
AT vonknoordegraafanton pulmonaryarterialhypertensioncombinedwithahighcardiacoutputstatethreeremarkablecases

Ejemplares similares