Prune Belly Syndrome Associated with Full Spectrum of VACTERL in a New Born

Prune belly syndrome (PBS) is a rare congenital anomaly of uncertain etiology. Many associations of PBS with other malformations were previously reported, but only few cases of the association with VACTERL have been described. We report a rare case of a Moroccan new born with PBS and complete VACTER...

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Autores principales: Younous, Said, Zarrouki, Youssef, Boutbaoucht, Mustapha, Mouaffak, Youssef, El Idrissi, Kawtar Ennour, Aboussair, Nissrine, Saiad, Mohammed O
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2012
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3761994/
https://www.ncbi.nlm.nih.gov/pubmed/24027688
http://dx.doi.org/10.4103/2249-4847.92234
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author Younous, Said
Zarrouki, Youssef
Boutbaoucht, Mustapha
Mouaffak, Youssef
El Idrissi, Kawtar Ennour
Aboussair, Nissrine
Saiad, Mohammed O
author_facet Younous, Said
Zarrouki, Youssef
Boutbaoucht, Mustapha
Mouaffak, Youssef
El Idrissi, Kawtar Ennour
Aboussair, Nissrine
Saiad, Mohammed O
author_sort Younous, Said
collection PubMed
description Prune belly syndrome (PBS) is a rare congenital anomaly of uncertain etiology. Many associations of PBS with other malformations were previously reported, but only few cases of the association with VACTERL have been described. We report a rare case of a Moroccan new born with PBS and complete VACTERL association. The cause of this association is still unknown, but a common etiology is possible, especially when for the two syndromes, a defect in mesodermal differentiation, in early first trimester, has been suggested.
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spelling pubmed-37619942013-09-11 Prune Belly Syndrome Associated with Full Spectrum of VACTERL in a New Born Younous, Said Zarrouki, Youssef Boutbaoucht, Mustapha Mouaffak, Youssef El Idrissi, Kawtar Ennour Aboussair, Nissrine Saiad, Mohammed O J Clin Neonatol Case Report Prune belly syndrome (PBS) is a rare congenital anomaly of uncertain etiology. Many associations of PBS with other malformations were previously reported, but only few cases of the association with VACTERL have been described. We report a rare case of a Moroccan new born with PBS and complete VACTERL association. The cause of this association is still unknown, but a common etiology is possible, especially when for the two syndromes, a defect in mesodermal differentiation, in early first trimester, has been suggested. Medknow Publications & Media Pvt Ltd 2012 /pmc/articles/PMC3761994/ /pubmed/24027688 http://dx.doi.org/10.4103/2249-4847.92234 Text en Copyright: © Journal of Clinical Neonatology http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Younous, Said
Zarrouki, Youssef
Boutbaoucht, Mustapha
Mouaffak, Youssef
El Idrissi, Kawtar Ennour
Aboussair, Nissrine
Saiad, Mohammed O
Prune Belly Syndrome Associated with Full Spectrum of VACTERL in a New Born
title Prune Belly Syndrome Associated with Full Spectrum of VACTERL in a New Born
title_full Prune Belly Syndrome Associated with Full Spectrum of VACTERL in a New Born
title_fullStr Prune Belly Syndrome Associated with Full Spectrum of VACTERL in a New Born
title_full_unstemmed Prune Belly Syndrome Associated with Full Spectrum of VACTERL in a New Born
title_short Prune Belly Syndrome Associated with Full Spectrum of VACTERL in a New Born
title_sort prune belly syndrome associated with full spectrum of vacterl in a new born
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3761994/
https://www.ncbi.nlm.nih.gov/pubmed/24027688
http://dx.doi.org/10.4103/2249-4847.92234
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