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Inflammatory myofibroblastic tumor with extensive involvement of the bladder in an adolescent: a case report

Inflammatory myofibroblastic tumor (IMT) is a rare lesion of unclear pathogenesis that shows a wide, highly variable spectrum of clinical behavior. We describe the case of a 17-year-old boy with a large IMT that infiltrated the bladder, ileocecal junction, peritoneum and pelvic retroperitoneal space...

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Detalles Bibliográficos
Autores principales: Yi, Xin Lin, Lu, Hao Yuan, Wu, Yue Xian, Li, Wen Hui, Meng, Qing Gui, Cheng, Ji Weng, Tang, Yong, Liu, Yu, Bai, Xian Zhong
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2013
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3765871/
https://www.ncbi.nlm.nih.gov/pubmed/23957966
http://dx.doi.org/10.1186/1477-7819-11-206
Descripción
Sumario:Inflammatory myofibroblastic tumor (IMT) is a rare lesion of unclear pathogenesis that shows a wide, highly variable spectrum of clinical behavior. We describe the case of a 17-year-old boy with a large IMT that infiltrated the bladder, ileocecal junction, peritoneum and pelvic retroperitoneal space. The tumor was associated with extensive toughening and thickening of the bladder, and, although it showed a tendency for invasive growth, it affected mainly the bladder and adjacent tissue. To the best of our knowledge, this case report is the first to describe an IMT involving the entire bladder and several adjacent pelviabdominal organs. The bladder wall was tough and could hardly be cut by scalpel. Levels of inflammatory response markers such as C-reactive protein fell after surgery.