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Topography of FUS pathology distinguishes late-onset BIBD from aFTLD-U

BACKGROUND: Multiple neurodegenerative diseases are characterized by the abnormal accumulation of FUS protein including various subtypes of frontotemporal lobar degeneration with FUS inclusions (FTLD-FUS). These subtypes include atypical frontotemporal lobar degeneration with ubiquitin-positive incl...

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Detalles Bibliográficos
Autores principales:	Lee, Edward B, Russ, Jenny, Jung, Hyunjoo, Elman, Lauren B, Chahine, Lama M, Kremens, Daniel, Miller, Bruce L, Coslett, H Branch, Trojanowski, John Q, Van Deerlin, Vivianna M, McCluskey, Leo F
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	BioMed Central 2013
Materias:	Research
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3767453/ https://www.ncbi.nlm.nih.gov/pubmed/24027631 http://dx.doi.org/10.1186/2051-5960-1-9

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