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Late-Onset Ornithine Carbamoyltransferase Deficiency Accompanying Acute Pancreatitis and Hyperammonemia

Hyperammonemia related to urea cycle disorders is a rare cause of potentially fatal encephalopathy that is encountered in intensive care units (ICUs). Left undiagnosed, this condition may manifest irreversible neuronal damage. However, timely diagnosis and treatment initiation can be facilitated sim...

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Detalles Bibliográficos
Autores principales:	Machado, Marcel Cerqueira Cesar, Fonseca, Gilton Marques, Jukemura, José
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Hindawi Publishing Corporation 2013
Materias:	Case Report
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3773375/ https://www.ncbi.nlm.nih.gov/pubmed/24073003 http://dx.doi.org/10.1155/2013/903546

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