Progressive Systemic Sclerosis in a Child

Systemic sclerosis is a clinically heterogeneous systemic disease affecting the connective tissues of skin, walls of blood vessels and internal organs like lung, heart and kidneys. Systemic sclerosis is very unusual in pediatric population. Children represent fewer than 10% of all cases. We report a...

Descripción completa

Detalles Bibliográficos
Autores principales: De, Arun K, Das, Kallol, Sil, Archan, Joardar, Swarnali
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2013
Materias:
E-Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3778798/
https://www.ncbi.nlm.nih.gov/pubmed/24082203
http://dx.doi.org/10.4103/0019-5154.117333
_version_ 1782285160640675840
author De, Arun K
Das, Kallol
Sil, Archan
Joardar, Swarnali
author_facet De, Arun K
Das, Kallol
Sil, Archan
Joardar, Swarnali
author_sort De, Arun K
collection PubMed
description Systemic sclerosis is a clinically heterogeneous systemic disease affecting the connective tissues of skin, walls of blood vessels and internal organs like lung, heart and kidneys. Systemic sclerosis is very unusual in pediatric population. Children represent fewer than 10% of all cases. We report a case of 11 years old girl of progressive systemic sclerosis presenting with features of cutaneous sclerosis, microstomia, mask-like facies, sclerodactyly, esophageal dysmotility, Raynaud's phenomenon, arthralgia and pulmonary fibrosis.
format Online
Article
Text
id pubmed-3778798
institution National Center for Biotechnology Information
language English
publishDate 2013
publisher Medknow Publications & Media Pvt Ltd
record_format MEDLINE/PubMed
spelling pubmed-37787982013-09-30 Progressive Systemic Sclerosis in a Child De, Arun K Das, Kallol Sil, Archan Joardar, Swarnali Indian J Dermatol E-Case Report Systemic sclerosis is a clinically heterogeneous systemic disease affecting the connective tissues of skin, walls of blood vessels and internal organs like lung, heart and kidneys. Systemic sclerosis is very unusual in pediatric population. Children represent fewer than 10% of all cases. We report a case of 11 years old girl of progressive systemic sclerosis presenting with features of cutaneous sclerosis, microstomia, mask-like facies, sclerodactyly, esophageal dysmotility, Raynaud's phenomenon, arthralgia and pulmonary fibrosis. Medknow Publications & Media Pvt Ltd 2013 /pmc/articles/PMC3778798/ /pubmed/24082203 http://dx.doi.org/10.4103/0019-5154.117333 Text en Copyright: © Indian Journal of Dermatology http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle E-Case Report
De, Arun K
Das, Kallol
Sil, Archan
Joardar, Swarnali
Progressive Systemic Sclerosis in a Child
title Progressive Systemic Sclerosis in a Child
title_full Progressive Systemic Sclerosis in a Child
title_fullStr Progressive Systemic Sclerosis in a Child
title_full_unstemmed Progressive Systemic Sclerosis in a Child
title_short Progressive Systemic Sclerosis in a Child
title_sort progressive systemic sclerosis in a child
topic E-Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3778798/
https://www.ncbi.nlm.nih.gov/pubmed/24082203
http://dx.doi.org/10.4103/0019-5154.117333
work_keys_str_mv AT dearunk progressivesystemicsclerosisinachild
AT daskallol progressivesystemicsclerosisinachild
AT silarchan progressivesystemicsclerosisinachild
AT joardarswarnali progressivesystemicsclerosisinachild

Ejemplares similares