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Bland-White-Garland syndrome – a rare and serious cause of failure to thrive

Patient: Male, 0 Final Diagnosis: Bland-White-Garland syndrome Symptoms: Cardiomegaly, feeding problems Medication: — Clinical Procedure: Reimplantation of the left coronary artery to the aorta Specialty: Pediatrics and Neonatology OBJECTIVE: Rare disease BACKGROUND: Bland-White-Garland syndrome (BW...

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Autores principales: Szmigielska, Agnieszka, Roszkowska-Blaim, Maria, Gołąbek-Dylewska, Małgorzata, Tomik, Agnieszka, Brzewski, Michał, Werner, Bożena
Formato: Online Artículo Texto
Lenguaje:English
Publicado: International Scientific Literature, Inc. 2013
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3783481/
https://www.ncbi.nlm.nih.gov/pubmed/24086793
http://dx.doi.org/10.12659/AJCR.889112
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author Szmigielska, Agnieszka
Roszkowska-Blaim, Maria
Gołąbek-Dylewska, Małgorzata
Tomik, Agnieszka
Brzewski, Michał
Werner, Bożena
author_facet Szmigielska, Agnieszka
Roszkowska-Blaim, Maria
Gołąbek-Dylewska, Małgorzata
Tomik, Agnieszka
Brzewski, Michał
Werner, Bożena
author_sort Szmigielska, Agnieszka
collection PubMed
description Patient: Male, 0 Final Diagnosis: Bland-White-Garland syndrome Symptoms: Cardiomegaly, feeding problems Medication: — Clinical Procedure: Reimplantation of the left coronary artery to the aorta Specialty: Pediatrics and Neonatology OBJECTIVE: Rare disease BACKGROUND: Bland-White-Garland syndrome (BWGS) is a very rare disease characterized by anomalous origin of the left coronary artery from the pulmonary trunk (ALCAPA). WBGS affects 1 in every 300 000 live births. Children typically present with dyspnea, pallor, and failure to thrive. Without surgical repair, most of these children die during the first months of life. CASE REPORT: This case report describes 3-month-old boy admitted to the hospital because of feeding problems. The boy was born at term, with birth weight 3200 g, and was 10 points in Apgar score. He was breast-fed from birth. From the seventh week of age, his mother observed his increasing difficulties with feeding. Physical examination revealed pale skin, diminished heart sounds, tachycardia, cardiomegaly, and hepatomegaly. Results of urine and blood tests and ultrasonography of the central nervous system and abdomen were normal. The chest radiography showed cardiomegaly and electrocardiogram revealed anterolateral myocardial infarction. On echocardiography, an anomalous left coronary artery arising from the pulmonary artery was found. The life-saving treatment of choice was immediate surgical reimplantation of the left coronary artery to the aorta. CONCLUSIONS: Children with congenital heart disease are often prone to malnutrition, but in rare cases failure to thrive and breast-feeding problems can be the first symptoms of life-threatening diseases like myocardial infarction secondary to Bland-White-Garland syndrome (BWGS).
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spelling pubmed-37834812013-10-01 Bland-White-Garland syndrome – a rare and serious cause of failure to thrive Szmigielska, Agnieszka Roszkowska-Blaim, Maria Gołąbek-Dylewska, Małgorzata Tomik, Agnieszka Brzewski, Michał Werner, Bożena Am J Case Rep Articles Patient: Male, 0 Final Diagnosis: Bland-White-Garland syndrome Symptoms: Cardiomegaly, feeding problems Medication: — Clinical Procedure: Reimplantation of the left coronary artery to the aorta Specialty: Pediatrics and Neonatology OBJECTIVE: Rare disease BACKGROUND: Bland-White-Garland syndrome (BWGS) is a very rare disease characterized by anomalous origin of the left coronary artery from the pulmonary trunk (ALCAPA). WBGS affects 1 in every 300 000 live births. Children typically present with dyspnea, pallor, and failure to thrive. Without surgical repair, most of these children die during the first months of life. CASE REPORT: This case report describes 3-month-old boy admitted to the hospital because of feeding problems. The boy was born at term, with birth weight 3200 g, and was 10 points in Apgar score. He was breast-fed from birth. From the seventh week of age, his mother observed his increasing difficulties with feeding. Physical examination revealed pale skin, diminished heart sounds, tachycardia, cardiomegaly, and hepatomegaly. Results of urine and blood tests and ultrasonography of the central nervous system and abdomen were normal. The chest radiography showed cardiomegaly and electrocardiogram revealed anterolateral myocardial infarction. On echocardiography, an anomalous left coronary artery arising from the pulmonary artery was found. The life-saving treatment of choice was immediate surgical reimplantation of the left coronary artery to the aorta. CONCLUSIONS: Children with congenital heart disease are often prone to malnutrition, but in rare cases failure to thrive and breast-feeding problems can be the first symptoms of life-threatening diseases like myocardial infarction secondary to Bland-White-Garland syndrome (BWGS). International Scientific Literature, Inc. 2013-09-16 /pmc/articles/PMC3783481/ /pubmed/24086793 http://dx.doi.org/10.12659/AJCR.889112 Text en © Am J Case Rep, 2013 This work is licensed under a Creative Commons Attribution-NonCommercial-NoDerivs 3.0 Unported License
spellingShingle Articles
Szmigielska, Agnieszka
Roszkowska-Blaim, Maria
Gołąbek-Dylewska, Małgorzata
Tomik, Agnieszka
Brzewski, Michał
Werner, Bożena
Bland-White-Garland syndrome – a rare and serious cause of failure to thrive
title Bland-White-Garland syndrome – a rare and serious cause of failure to thrive
title_full Bland-White-Garland syndrome – a rare and serious cause of failure to thrive
title_fullStr Bland-White-Garland syndrome – a rare and serious cause of failure to thrive
title_full_unstemmed Bland-White-Garland syndrome – a rare and serious cause of failure to thrive
title_short Bland-White-Garland syndrome – a rare and serious cause of failure to thrive
title_sort bland-white-garland syndrome – a rare and serious cause of failure to thrive
topic Articles
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3783481/
https://www.ncbi.nlm.nih.gov/pubmed/24086793
http://dx.doi.org/10.12659/AJCR.889112
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