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DNA Damage Responses and Oxidative Stress in Dyskeratosis Congenita

Dyskeratosis congenita (DC) is an inherited multisystem disorder of premature aging, cancer predisposition, and bone marrow failure caused by selective exhaustion of highly proliferative cell pools. DC patients also have a poor tolerance to chemo/radiotherapy and bone marrow transplantation. Althoug...

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Detalles Bibliográficos
Autores principales:	Pereboeva, Larisa, Westin, Erik, Patel, Toral, Flaniken, Ian, Lamb, Lawrence, Klingelhutz, Aloysius, Goldman, Frederick
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Public Library of Science 2013
Materias:	Research Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3790691/ https://www.ncbi.nlm.nih.gov/pubmed/24124565 http://dx.doi.org/10.1371/journal.pone.0076473

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