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Proteome adaptations in Ethe1-deficient mice indicate a role in lipid catabolism and cytoskeleton organization via post-translational protein modifications
Hydrogen sulfide is a physiologically relevant signalling molecule. However, circulating levels of this highly biologically active substance have to be maintained within tightly controlled limits in order to avoid toxic side effects. In patients suffering from EE (ethylmalonic encephalopathy), a blo...
Autores principales: | Hildebrandt, Tatjana M., Di Meo, Ivano, Zeviani, Massimo, Viscomi, Carlo, Braun, Hans-Peter |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Portland Press Ltd.
2013
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3827611/ https://www.ncbi.nlm.nih.gov/pubmed/23800285 http://dx.doi.org/10.1042/BSR20130051 |
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