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Vanished Kidney by Pheripheral Nerve Seath Tumor: A Rare Case Report

Malignant peripheral nerve-sheath tumor (MPNST) is a high-grade malignant tumor of ecto-mesenchymal origin comprising approximately 10% of soft-tissue sarcomas. They tend to occur associated with neurofibromatosis or sporadically. Here we report a MPNST at an extremely rare location and behavior cau...

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Detalles Bibliográficos
Autores principales: Rai Bansal, Anand, Singh Griwan, Mahavir, Rajan Karthikeyan, Yayathi, Kumar Singh, Santosh
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Kowsar 2013
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3830914/
https://www.ncbi.nlm.nih.gov/pubmed/24282798
http://dx.doi.org/10.5812/numonthly.8029
Descripción
Sumario:Malignant peripheral nerve-sheath tumor (MPNST) is a high-grade malignant tumor of ecto-mesenchymal origin comprising approximately 10% of soft-tissue sarcomas. They tend to occur associated with neurofibromatosis or sporadically. Here we report a MPNST at an extremely rare location and behavior causing disappearance of the entire kidney. Patient evaluation included clinical, biochemical and radiological studies before treatment. Histological study revealed the rare diagnosis. Patient was asymptomatic at six-month follow-up after treatment.