A case of pulmonary alveolar proteinosis treated with whole lung lavage

Pulmonary alveolar proteinosis represents a rare syndrome characterized by the accumulation of proteinaceous phospholipid-laden material in the alveoli. This leads to impaired gas exchange and arterial hypoxemia of varying degrees. The diagnosis is confirmed by lung biopsy. Sequential whole-lung lav...

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Detalles Bibliográficos
Autores principales: Bansal, Avdhesh, Sikri, Vikas
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2013
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3841497/
https://www.ncbi.nlm.nih.gov/pubmed/24339646
http://dx.doi.org/10.4103/0972-5229.120327
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author Bansal, Avdhesh
Sikri, Vikas
author_facet Bansal, Avdhesh
Sikri, Vikas
author_sort Bansal, Avdhesh
collection PubMed
description Pulmonary alveolar proteinosis represents a rare syndrome characterized by the accumulation of proteinaceous phospholipid-laden material in the alveoli. This leads to impaired gas exchange and arterial hypoxemia of varying degrees. The diagnosis is confirmed by lung biopsy. Sequential whole-lung lavage (WLL) first described in 1963 is the standard of care. We report a case of a male diagnosed of having pulmonary alveolar proteinosis (PAP) on transbroncial lung biopsy (TBLB). He was treated with sequential WLL (Left followed by right, Left being more involved on chest X-ray) followed by recombinant GM-CSF, with good result.
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spelling pubmed-38414972013-12-11 A case of pulmonary alveolar proteinosis treated with whole lung lavage Bansal, Avdhesh Sikri, Vikas Indian J Crit Care Med Case Report Pulmonary alveolar proteinosis represents a rare syndrome characterized by the accumulation of proteinaceous phospholipid-laden material in the alveoli. This leads to impaired gas exchange and arterial hypoxemia of varying degrees. The diagnosis is confirmed by lung biopsy. Sequential whole-lung lavage (WLL) first described in 1963 is the standard of care. We report a case of a male diagnosed of having pulmonary alveolar proteinosis (PAP) on transbroncial lung biopsy (TBLB). He was treated with sequential WLL (Left followed by right, Left being more involved on chest X-ray) followed by recombinant GM-CSF, with good result. Medknow Publications & Media Pvt Ltd 2013 /pmc/articles/PMC3841497/ /pubmed/24339646 http://dx.doi.org/10.4103/0972-5229.120327 Text en Copyright: © Indian Journal of Critical Care Medicine http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Bansal, Avdhesh
Sikri, Vikas
A case of pulmonary alveolar proteinosis treated with whole lung lavage
title A case of pulmonary alveolar proteinosis treated with whole lung lavage
title_full A case of pulmonary alveolar proteinosis treated with whole lung lavage
title_fullStr A case of pulmonary alveolar proteinosis treated with whole lung lavage
title_full_unstemmed A case of pulmonary alveolar proteinosis treated with whole lung lavage
title_short A case of pulmonary alveolar proteinosis treated with whole lung lavage
title_sort case of pulmonary alveolar proteinosis treated with whole lung lavage
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3841497/
https://www.ncbi.nlm.nih.gov/pubmed/24339646
http://dx.doi.org/10.4103/0972-5229.120327
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