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Observational Cohort Study of Ventricular Arrhythmia in Adults with Marfan Syndrome Caused by FBN1 Mutations

BACKGROUND: Marfan syndrome is associated with ventricular arrhythmia but risk factors including FBN1 mutation characteristics require elucidation. METHODS AND RESULTS: We performed an observational cohort study of 80 consecutive adults (30 men, 50 women aged 42±15 years) with Marfan syndrome caused...

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Detalles Bibliográficos
Autores principales:	Aydin, Ali, Adsay, Baran A., Sheikhzadeh, Sara, Keyser, Britta, Rybczynski, Meike, Sondermann, Claudia, Detter, Christian, Steven, Daniel, Robinson, Peter N., Berger, Jürgen, Schmidtke, Jörg, Blankenberg, Stefan, Willems, Stephan, von Kodolitsch, Yskert, Hoffmann, Boris A.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Public Library of Science 2013
Materias:	Research Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3862481/ https://www.ncbi.nlm.nih.gov/pubmed/24349050 http://dx.doi.org/10.1371/journal.pone.0081281

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