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Primary Carnitine Deficiency and Cardiomyopathy
Carnitine is essential for the transfer of long-chain fatty acids from the cytosol into mitochondria for subsequent β-oxidation. A lack of carnitine results in impaired energy production from long-chain fatty acids, especially during periods of fasting or stress. Primary carnitine deficiency (PCD) i...
Autores principales: | Fu, Lijun, Huang, Meirong, Chen, Shubao |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
The Korean Society of Cardiology
2013
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3875693/ https://www.ncbi.nlm.nih.gov/pubmed/24385988 http://dx.doi.org/10.4070/kcj.2013.43.12.785 |
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