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Phacomatosis pigmentovascularis type IIa - Case report

Phacomatosis Pigmentovascularis is a rare syndrome characterized by capillary malformation and pigmentary nevus. A case of a 2-year-old patient is reported, who presented extensive nevus flammeus and an aberrant Mongolian spot, without systemic disease, manifestations that allow us to classify this...

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Detalles Bibliográficos
Autores principales: Segatto, Majoriê Mergen, Schmitt, Eloísa Unfer, Hagemann, Laura Netto, da Silva, Roberta Castilhos, Cattani, Cristiane Almeida Soares
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Sociedade Brasileira de Dermatologia 2013
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3875999/
https://www.ncbi.nlm.nih.gov/pubmed/24346888
http://dx.doi.org/10.1590/abd1806-4841.20132248
Descripción
Sumario:Phacomatosis Pigmentovascularis is a rare syndrome characterized by capillary malformation and pigmentary nevus. A case of a 2-year-old patient is reported, who presented extensive nevus flammeus and an aberrant Mongolian spot, without systemic disease, manifestations that allow us to classify this case as type IIa Phacomatosis Pigmentovascularis, according to Hasegawa's classification.