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Olfactory Deficits in Niemann-Pick Type C1 (NPC1) Disease

BACKGROUND: Niemann-Pick type C disease (NPC) is a rare autosomal recessive lipid storage disease characterized by progressive neurodegeneration. As only a few studies have been conducted on the impact of NPC on sensory systems, we used a mutant mouse model (NPC1(−/−)) to examine the effects of this...

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Detalles Bibliográficos
Autores principales:	Hovakimyan, Marina, Meyer, Anja, Lukas, Jan, Luo, Jiankai, Gudziol, Volker, Hummel, Thomas, Rolfs, Arndt, Wree, Andreas, Witt, Martin
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Public Library of Science 2013
Materias:	Research Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3877006/ https://www.ncbi.nlm.nih.gov/pubmed/24391715 http://dx.doi.org/10.1371/journal.pone.0082216

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