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A Case of Ichthyosis Hystrix: Unusual Manifestation of This Rare Disease

Ichthyosis hystrix is a term used to describe an ichthyosiform dermatosis which is characterized by hyperkeratotic spiny scales mainly over extensor aspects of limbs with palmoplantar keratoderma and occasionally associated with deafness and neurological deficit. It is a rare autosomal dominant form...

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Autores principales: Biswas, Projna, De, Abhishek, Sendur, Sampreeti, Nag, Falguni, Saha, Archana, Chatterjee, Gobinda
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2014
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3884936/
https://www.ncbi.nlm.nih.gov/pubmed/24470668
http://dx.doi.org/10.4103/0019-5154.123512
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author Biswas, Projna
De, Abhishek
Sendur, Sampreeti
Nag, Falguni
Saha, Archana
Chatterjee, Gobinda
author_facet Biswas, Projna
De, Abhishek
Sendur, Sampreeti
Nag, Falguni
Saha, Archana
Chatterjee, Gobinda
author_sort Biswas, Projna
collection PubMed
description Ichthyosis hystrix is a term used to describe an ichthyosiform dermatosis which is characterized by hyperkeratotic spiny scales mainly over extensor aspects of limbs with palmoplantar keratoderma and occasionally associated with deafness and neurological deficit. It is a rare autosomal dominant form of ichthyosis and very few cases are reported in literature. We are presenting a 46 years-old-male patient of ichthyosis hystrix with unusual presentation. He had lesions mainly over the face and scalp with palmoplantar keratoderma and significant nail changes.
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spelling pubmed-38849362014-01-27 A Case of Ichthyosis Hystrix: Unusual Manifestation of This Rare Disease Biswas, Projna De, Abhishek Sendur, Sampreeti Nag, Falguni Saha, Archana Chatterjee, Gobinda Indian J Dermatol Case Report Ichthyosis hystrix is a term used to describe an ichthyosiform dermatosis which is characterized by hyperkeratotic spiny scales mainly over extensor aspects of limbs with palmoplantar keratoderma and occasionally associated with deafness and neurological deficit. It is a rare autosomal dominant form of ichthyosis and very few cases are reported in literature. We are presenting a 46 years-old-male patient of ichthyosis hystrix with unusual presentation. He had lesions mainly over the face and scalp with palmoplantar keratoderma and significant nail changes. Medknow Publications & Media Pvt Ltd 2014 /pmc/articles/PMC3884936/ /pubmed/24470668 http://dx.doi.org/10.4103/0019-5154.123512 Text en Copyright: © Indian Journal of Dermatology http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Biswas, Projna
De, Abhishek
Sendur, Sampreeti
Nag, Falguni
Saha, Archana
Chatterjee, Gobinda
A Case of Ichthyosis Hystrix: Unusual Manifestation of This Rare Disease
title A Case of Ichthyosis Hystrix: Unusual Manifestation of This Rare Disease
title_full A Case of Ichthyosis Hystrix: Unusual Manifestation of This Rare Disease
title_fullStr A Case of Ichthyosis Hystrix: Unusual Manifestation of This Rare Disease
title_full_unstemmed A Case of Ichthyosis Hystrix: Unusual Manifestation of This Rare Disease
title_short A Case of Ichthyosis Hystrix: Unusual Manifestation of This Rare Disease
title_sort case of ichthyosis hystrix: unusual manifestation of this rare disease
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3884936/
https://www.ncbi.nlm.nih.gov/pubmed/24470668
http://dx.doi.org/10.4103/0019-5154.123512
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