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Angiokeratoma Circumscriptum in a Young Male
A 20-year-old male presented with multiple eruptions on his right leg since birth; these bled and were painful on trivial trauma. Examination revealed dark brown, hyperkeratotic, indurated, verrucous linear plaques with irregular borders. Histopathological evidence of hyperkeratosis, acanthosis, and...
Autores principales: | , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Medknow Publications & Media Pvt Ltd
2014
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3884937/ https://www.ncbi.nlm.nih.gov/pubmed/24470669 http://dx.doi.org/10.4103/0019-5154.123514 |
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author | Sadana, Dinkar Sharma, Yugal K Dash, Kedarnath Chaudhari, Nitin D Dharwadkar, Arpana Anil Dogra, Bharat B |
author_facet | Sadana, Dinkar Sharma, Yugal K Dash, Kedarnath Chaudhari, Nitin D Dharwadkar, Arpana Anil Dogra, Bharat B |
author_sort | Sadana, Dinkar |
collection | PubMed |
description | A 20-year-old male presented with multiple eruptions on his right leg since birth; these bled and were painful on trivial trauma. Examination revealed dark brown, hyperkeratotic, indurated, verrucous linear plaques with irregular borders. Histopathological evidence of hyperkeratosis, acanthosis, and extensive vascular proliferation in papillary dermis confirmed clinical suspicion of angiokeratoma circumscriptum (AKC). Excision and skin grafting yielded a cosmetically favorable outcome. Angiokeratomas, first described by Mibeli in 1889, are a group of vascular ectasias involving the papillary dermis. Angiokeratomas are more common in males; however, AKC–the rarest of its five variants–exhibits a female preponderance (F:M:3:1). AKC is an extremely rare nevoid disorder, only 100 of its cases having been reported in the world literature until 2006. Herein, we have reported a typical case of AKC in a young male that was previously misdiagnosed, and the patient wrongly counseled about the likelihood of its spontaneous regression. |
format | Online Article Text |
id | pubmed-3884937 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2014 |
publisher | Medknow Publications & Media Pvt Ltd |
record_format | MEDLINE/PubMed |
spelling | pubmed-38849372014-01-27 Angiokeratoma Circumscriptum in a Young Male Sadana, Dinkar Sharma, Yugal K Dash, Kedarnath Chaudhari, Nitin D Dharwadkar, Arpana Anil Dogra, Bharat B Indian J Dermatol Case Report A 20-year-old male presented with multiple eruptions on his right leg since birth; these bled and were painful on trivial trauma. Examination revealed dark brown, hyperkeratotic, indurated, verrucous linear plaques with irregular borders. Histopathological evidence of hyperkeratosis, acanthosis, and extensive vascular proliferation in papillary dermis confirmed clinical suspicion of angiokeratoma circumscriptum (AKC). Excision and skin grafting yielded a cosmetically favorable outcome. Angiokeratomas, first described by Mibeli in 1889, are a group of vascular ectasias involving the papillary dermis. Angiokeratomas are more common in males; however, AKC–the rarest of its five variants–exhibits a female preponderance (F:M:3:1). AKC is an extremely rare nevoid disorder, only 100 of its cases having been reported in the world literature until 2006. Herein, we have reported a typical case of AKC in a young male that was previously misdiagnosed, and the patient wrongly counseled about the likelihood of its spontaneous regression. Medknow Publications & Media Pvt Ltd 2014 /pmc/articles/PMC3884937/ /pubmed/24470669 http://dx.doi.org/10.4103/0019-5154.123514 Text en Copyright: © Indian Journal of Dermatology http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Sadana, Dinkar Sharma, Yugal K Dash, Kedarnath Chaudhari, Nitin D Dharwadkar, Arpana Anil Dogra, Bharat B Angiokeratoma Circumscriptum in a Young Male |
title | Angiokeratoma Circumscriptum in a Young Male |
title_full | Angiokeratoma Circumscriptum in a Young Male |
title_fullStr | Angiokeratoma Circumscriptum in a Young Male |
title_full_unstemmed | Angiokeratoma Circumscriptum in a Young Male |
title_short | Angiokeratoma Circumscriptum in a Young Male |
title_sort | angiokeratoma circumscriptum in a young male |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3884937/ https://www.ncbi.nlm.nih.gov/pubmed/24470669 http://dx.doi.org/10.4103/0019-5154.123514 |
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