PEComa: A Perivascular Epithelioid Cell Tumor in the Liver—A Case Report and Review of the Literature

Perivascular epithelioid cell tumors are soft tissue tumors that can occur in various locations in the body whose incidence is rising. Hepatic PEComas are quite rare and diagnosis involves positivity of Melan-A and HMB45 on immunohistochemistry. Usual treatment is surgery for benign tumors and chemo...

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Autores principales: Khaja, Faseeh, Carilli, Allison, Baidas, Said, Sriharan, Aravindhan, Norford, Shanedelle
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi Publishing Corporation 2013
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3891746/
https://www.ncbi.nlm.nih.gov/pubmed/24489554
http://dx.doi.org/10.1155/2013/904126
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author Khaja, Faseeh
Carilli, Allison
Baidas, Said
Sriharan, Aravindhan
Norford, Shanedelle
author_facet Khaja, Faseeh
Carilli, Allison
Baidas, Said
Sriharan, Aravindhan
Norford, Shanedelle
author_sort Khaja, Faseeh
collection PubMed
description Perivascular epithelioid cell tumors are soft tissue tumors that can occur in various locations in the body whose incidence is rising. Hepatic PEComas are quite rare and diagnosis involves positivity of Melan-A and HMB45 on immunohistochemistry. Usual treatment is surgery for benign tumors and chemotherapy including mTOR inhibitors for malignant tumors. Here we discuss the radiological and pathological diagnosis, evaluation, and management of a hepatic PEComa. We describe a 51-year-old patient who was diagnosed incidentally after unusual physical exam findings.
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spelling pubmed-38917462014-02-02 PEComa: A Perivascular Epithelioid Cell Tumor in the Liver—A Case Report and Review of the Literature Khaja, Faseeh Carilli, Allison Baidas, Said Sriharan, Aravindhan Norford, Shanedelle Case Rep Med Case Report Perivascular epithelioid cell tumors are soft tissue tumors that can occur in various locations in the body whose incidence is rising. Hepatic PEComas are quite rare and diagnosis involves positivity of Melan-A and HMB45 on immunohistochemistry. Usual treatment is surgery for benign tumors and chemotherapy including mTOR inhibitors for malignant tumors. Here we discuss the radiological and pathological diagnosis, evaluation, and management of a hepatic PEComa. We describe a 51-year-old patient who was diagnosed incidentally after unusual physical exam findings. Hindawi Publishing Corporation 2013 2013-12-29 /pmc/articles/PMC3891746/ /pubmed/24489554 http://dx.doi.org/10.1155/2013/904126 Text en Copyright © 2013 Faseeh Khaja et al. https://creativecommons.org/licenses/by/3.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Khaja, Faseeh
Carilli, Allison
Baidas, Said
Sriharan, Aravindhan
Norford, Shanedelle
PEComa: A Perivascular Epithelioid Cell Tumor in the Liver—A Case Report and Review of the Literature
title PEComa: A Perivascular Epithelioid Cell Tumor in the Liver—A Case Report and Review of the Literature
title_full PEComa: A Perivascular Epithelioid Cell Tumor in the Liver—A Case Report and Review of the Literature
title_fullStr PEComa: A Perivascular Epithelioid Cell Tumor in the Liver—A Case Report and Review of the Literature
title_full_unstemmed PEComa: A Perivascular Epithelioid Cell Tumor in the Liver—A Case Report and Review of the Literature
title_short PEComa: A Perivascular Epithelioid Cell Tumor in the Liver—A Case Report and Review of the Literature
title_sort pecoma: a perivascular epithelioid cell tumor in the liver—a case report and review of the literature
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3891746/
https://www.ncbi.nlm.nih.gov/pubmed/24489554
http://dx.doi.org/10.1155/2013/904126
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AT baidassaid pecomaaperivascularepithelioidcelltumorintheliveracasereportandreviewoftheliterature
AT sriharanaravindhan pecomaaperivascularepithelioidcelltumorintheliveracasereportandreviewoftheliterature
AT norfordshanedelle pecomaaperivascularepithelioidcelltumorintheliveracasereportandreviewoftheliterature

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