Liver Abscesses and Hyper IgM Syndrome

Hyper IgM (HIGM) syndrome is an immunodeficiency that can lead to liver disease in more than 80% of affected males by an age of 20 years. Hepatitis, sclerosing cholangitis, and hepatocellular malignancies are common among them. We encountered two cases in children of less than 12 years who presented...

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Autores principales: Shah, Ira, Rahangdale, Aarti, Bhatnagar, Sushmita
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2013
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3894042/
https://www.ncbi.nlm.nih.gov/pubmed/24479081
http://dx.doi.org/10.4103/2249-4863.117429
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author Shah, Ira
Rahangdale, Aarti
Bhatnagar, Sushmita
author_facet Shah, Ira
Rahangdale, Aarti
Bhatnagar, Sushmita
author_sort Shah, Ira
collection PubMed
description Hyper IgM (HIGM) syndrome is an immunodeficiency that can lead to liver disease in more than 80% of affected males by an age of 20 years. Hepatitis, sclerosing cholangitis, and hepatocellular malignancies are common among them. We encountered two cases in children of less than 12 years who presented with typical manifestations of liver abscess and were later detected to have a concomitant underlying HIGM syndrome.
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spelling pubmed-38940422014-01-29 Liver Abscesses and Hyper IgM Syndrome Shah, Ira Rahangdale, Aarti Bhatnagar, Sushmita J Family Med Prim Care Case Report Hyper IgM (HIGM) syndrome is an immunodeficiency that can lead to liver disease in more than 80% of affected males by an age of 20 years. Hepatitis, sclerosing cholangitis, and hepatocellular malignancies are common among them. We encountered two cases in children of less than 12 years who presented with typical manifestations of liver abscess and were later detected to have a concomitant underlying HIGM syndrome. Medknow Publications & Media Pvt Ltd 2013 /pmc/articles/PMC3894042/ /pubmed/24479081 http://dx.doi.org/10.4103/2249-4863.117429 Text en Copyright: © Journal of Family Medicine and Primary Care http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Shah, Ira
Rahangdale, Aarti
Bhatnagar, Sushmita
Liver Abscesses and Hyper IgM Syndrome
title Liver Abscesses and Hyper IgM Syndrome
title_full Liver Abscesses and Hyper IgM Syndrome
title_fullStr Liver Abscesses and Hyper IgM Syndrome
title_full_unstemmed Liver Abscesses and Hyper IgM Syndrome
title_short Liver Abscesses and Hyper IgM Syndrome
title_sort liver abscesses and hyper igm syndrome
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3894042/
https://www.ncbi.nlm.nih.gov/pubmed/24479081
http://dx.doi.org/10.4103/2249-4863.117429
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