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Complex I Function and Supercomplex Formation Are Preserved in Liver Mitochondria Despite Progressive Complex III Deficiency

Functional oxidative phosphorylation requires appropriately assembled mitochondrial respiratory complexes and their supercomplexes formed mainly of complexes I, III and IV. BCS1L is the chaperone needed to incorporate the catalytic subunit, Rieske iron-sulfur protein, into complex III at the final s...

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Detalles Bibliográficos
Autores principales:	Davoudi, Mina, Kotarsky, Heike, Hansson, Eva, Fellman, Vineta
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Public Library of Science 2014
Materias:	Research Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3899299/ https://www.ncbi.nlm.nih.gov/pubmed/24466228 http://dx.doi.org/10.1371/journal.pone.0086767

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