Giant orbital oncocytoma

BACKGROUND AND IMPORTANCE: Oncocytomas are rare benign tumours often arising from the lacrimal or salivary glands, usually small in size. CLINICAL PRESENTATION: We report a giant unilateral orbital oncocytoma in a 19-year-old male from Papua New Guinea, presenting with progressive proptosis-threatening vision. Due to retro-ocular extension of the lesion, surgical excision was performed via a fronto-orbitozygomatic craniotomy and orbitotomy. A sub-total excision of the lesion was achieved, with overall improvement in proptosis and cosmesis. CONCLUSION: This appears to be the first documented case of a giant intra-orbital oncocytoma being resected neurosurgically via craniotomy.