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Non-familial cherubism: A case report with its surgical management

Cherubism is an autosomal-dominant inherited syndrome; it starts in early childhood and involutes by puberty. It is characterized by excessive bone degradation of the jaws and development of fibrous tissue masses. Non-familial cherubism is a rare entity, which needs to be documented. This paper desc...

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Detalles Bibliográficos
Autores principales: Hungund, Shital A., Singh, Vatsala, Nagaraja, Chaitra
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2013
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3917218/
https://www.ncbi.nlm.nih.gov/pubmed/24554898
http://dx.doi.org/10.4103/0972-124X.124532
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author Hungund, Shital A.
Singh, Vatsala
Nagaraja, Chaitra
author_facet Hungund, Shital A.
Singh, Vatsala
Nagaraja, Chaitra
author_sort Hungund, Shital A.
collection PubMed
description Cherubism is an autosomal-dominant inherited syndrome; it starts in early childhood and involutes by puberty. It is characterized by excessive bone degradation of the jaws and development of fibrous tissue masses. Non-familial cherubism is a rare entity, which needs to be documented. This paper describes the findings of non-familial cherubism. An 11-year-old male patient reported with bilateral swellings of the jaws and unerupted teeth. Extensive gingival overgrowth, cherubic facial appearance, multilocular osteolytic lesions in radiographs and family history lead to the diagnosis of non-familial cherubism. Treatment included full mouth excision of the gingival tissue by gingivectomy with both manual instrumentation and electrosurgery. Patient is being monitored and recalled for frequent follow-ups. Dental practitioners need to be alert with patients presenting with gingival overgrowth.
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spelling pubmed-39172182014-02-19 Non-familial cherubism: A case report with its surgical management Hungund, Shital A. Singh, Vatsala Nagaraja, Chaitra J Indian Soc Periodontol Case Report Cherubism is an autosomal-dominant inherited syndrome; it starts in early childhood and involutes by puberty. It is characterized by excessive bone degradation of the jaws and development of fibrous tissue masses. Non-familial cherubism is a rare entity, which needs to be documented. This paper describes the findings of non-familial cherubism. An 11-year-old male patient reported with bilateral swellings of the jaws and unerupted teeth. Extensive gingival overgrowth, cherubic facial appearance, multilocular osteolytic lesions in radiographs and family history lead to the diagnosis of non-familial cherubism. Treatment included full mouth excision of the gingival tissue by gingivectomy with both manual instrumentation and electrosurgery. Patient is being monitored and recalled for frequent follow-ups. Dental practitioners need to be alert with patients presenting with gingival overgrowth. Medknow Publications & Media Pvt Ltd 2013 /pmc/articles/PMC3917218/ /pubmed/24554898 http://dx.doi.org/10.4103/0972-124X.124532 Text en Copyright: © Journal of Indian Society of Periodontology http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Hungund, Shital A.
Singh, Vatsala
Nagaraja, Chaitra
Non-familial cherubism: A case report with its surgical management
title Non-familial cherubism: A case report with its surgical management
title_full Non-familial cherubism: A case report with its surgical management
title_fullStr Non-familial cherubism: A case report with its surgical management
title_full_unstemmed Non-familial cherubism: A case report with its surgical management
title_short Non-familial cherubism: A case report with its surgical management
title_sort non-familial cherubism: a case report with its surgical management
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3917218/
https://www.ncbi.nlm.nih.gov/pubmed/24554898
http://dx.doi.org/10.4103/0972-124X.124532
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