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Non-familial cherubism: A case report with its surgical management
Cherubism is an autosomal-dominant inherited syndrome; it starts in early childhood and involutes by puberty. It is characterized by excessive bone degradation of the jaws and development of fibrous tissue masses. Non-familial cherubism is a rare entity, which needs to be documented. This paper desc...
Autores principales: | , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
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Medknow Publications & Media Pvt Ltd
2013
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Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3917218/ https://www.ncbi.nlm.nih.gov/pubmed/24554898 http://dx.doi.org/10.4103/0972-124X.124532 |
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author | Hungund, Shital A. Singh, Vatsala Nagaraja, Chaitra |
author_facet | Hungund, Shital A. Singh, Vatsala Nagaraja, Chaitra |
author_sort | Hungund, Shital A. |
collection | PubMed |
description | Cherubism is an autosomal-dominant inherited syndrome; it starts in early childhood and involutes by puberty. It is characterized by excessive bone degradation of the jaws and development of fibrous tissue masses. Non-familial cherubism is a rare entity, which needs to be documented. This paper describes the findings of non-familial cherubism. An 11-year-old male patient reported with bilateral swellings of the jaws and unerupted teeth. Extensive gingival overgrowth, cherubic facial appearance, multilocular osteolytic lesions in radiographs and family history lead to the diagnosis of non-familial cherubism. Treatment included full mouth excision of the gingival tissue by gingivectomy with both manual instrumentation and electrosurgery. Patient is being monitored and recalled for frequent follow-ups. Dental practitioners need to be alert with patients presenting with gingival overgrowth. |
format | Online Article Text |
id | pubmed-3917218 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2013 |
publisher | Medknow Publications & Media Pvt Ltd |
record_format | MEDLINE/PubMed |
spelling | pubmed-39172182014-02-19 Non-familial cherubism: A case report with its surgical management Hungund, Shital A. Singh, Vatsala Nagaraja, Chaitra J Indian Soc Periodontol Case Report Cherubism is an autosomal-dominant inherited syndrome; it starts in early childhood and involutes by puberty. It is characterized by excessive bone degradation of the jaws and development of fibrous tissue masses. Non-familial cherubism is a rare entity, which needs to be documented. This paper describes the findings of non-familial cherubism. An 11-year-old male patient reported with bilateral swellings of the jaws and unerupted teeth. Extensive gingival overgrowth, cherubic facial appearance, multilocular osteolytic lesions in radiographs and family history lead to the diagnosis of non-familial cherubism. Treatment included full mouth excision of the gingival tissue by gingivectomy with both manual instrumentation and electrosurgery. Patient is being monitored and recalled for frequent follow-ups. Dental practitioners need to be alert with patients presenting with gingival overgrowth. Medknow Publications & Media Pvt Ltd 2013 /pmc/articles/PMC3917218/ /pubmed/24554898 http://dx.doi.org/10.4103/0972-124X.124532 Text en Copyright: © Journal of Indian Society of Periodontology http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Hungund, Shital A. Singh, Vatsala Nagaraja, Chaitra Non-familial cherubism: A case report with its surgical management |
title | Non-familial cherubism: A case report with its surgical management |
title_full | Non-familial cherubism: A case report with its surgical management |
title_fullStr | Non-familial cherubism: A case report with its surgical management |
title_full_unstemmed | Non-familial cherubism: A case report with its surgical management |
title_short | Non-familial cherubism: A case report with its surgical management |
title_sort | non-familial cherubism: a case report with its surgical management |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3917218/ https://www.ncbi.nlm.nih.gov/pubmed/24554898 http://dx.doi.org/10.4103/0972-124X.124532 |
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