The obstructive siblings: Relapsing polychondritis without chondritis?

Progressive narrowing of the central airways due to diffuse inflammation is a potential life-threatening condition. A number of diseases have been described as possible causes. We present two siblings with severe central airway obstruction. Despite considerable efforts we have not been able to match...

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Detalles Bibliográficos
Autores principales: Sæverud, Haavard A., Borchsenius, F., Mellem, H., Finstad, P., Skjønsberg, Ole H.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2013
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3920352/
https://www.ncbi.nlm.nih.gov/pubmed/26029500
http://dx.doi.org/10.1016/j.rmcr.2013.04.005
Descripción
Sumario:Progressive narrowing of the central airways due to diffuse inflammation is a potential life-threatening condition. A number of diseases have been described as possible causes. We present two siblings with severe central airway obstruction. Despite considerable efforts we have not been able to match the clinical appearance of our patients with the diagnostic criteria of any of the disease entities known to cause this condition.

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