Krukenberg tumour as the initial presentation of Peutz-Jeghers syndrome

Peutz-Jeghers syndrome (PJS) is an hereditary syndrome characterized by gastrointestinal polyposis and mucocutaneous pigmentation. PJS patients are at increased risk of developing various cancers, especially of the gastrointestinal and gynaecological tracts. Colonic adenocarcinoma is one of the more...

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Detalles Bibliográficos
Autores principales: Remalayam, Bhavith, Kuriakose, Santhosh, Kambarath, Prathapan Valiya, Mavali, Ramachandran Thazhath
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Oxford University Press 2014
Materias:
Case Reports
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3920993/
https://www.ncbi.nlm.nih.gov/pubmed/24760241
http://dx.doi.org/10.1093/gastro/got031
Descripción
Sumario:Peutz-Jeghers syndrome (PJS) is an hereditary syndrome characterized by gastrointestinal polyposis and mucocutaneous pigmentation. PJS patients are at increased risk of developing various cancers, especially of the gastrointestinal and gynaecological tracts. Colonic adenocarcinoma is one of the more common tumours that occur in PJS. We report a young lady presenting with a large ovarian tumour, later diagnosed to have PJS with colonic signet cell adenocarcinoma and synchronous ovarian metastasis.

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