Krukenberg tumour as the initial presentation of Peutz-Jeghers syndrome

Peutz-Jeghers syndrome (PJS) is an hereditary syndrome characterized by gastrointestinal polyposis and mucocutaneous pigmentation. PJS patients are at increased risk of developing various cancers, especially of the gastrointestinal and gynaecological tracts. Colonic adenocarcinoma is one of the more...

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Autores principales: Remalayam, Bhavith, Kuriakose, Santhosh, Kambarath, Prathapan Valiya, Mavali, Ramachandran Thazhath
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Oxford University Press 2014
Materias:
Case Reports
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3920993/
https://www.ncbi.nlm.nih.gov/pubmed/24760241
http://dx.doi.org/10.1093/gastro/got031
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author Remalayam, Bhavith
Kuriakose, Santhosh
Kambarath, Prathapan Valiya
Mavali, Ramachandran Thazhath
author_facet Remalayam, Bhavith
Kuriakose, Santhosh
Kambarath, Prathapan Valiya
Mavali, Ramachandran Thazhath
author_sort Remalayam, Bhavith
collection PubMed
description Peutz-Jeghers syndrome (PJS) is an hereditary syndrome characterized by gastrointestinal polyposis and mucocutaneous pigmentation. PJS patients are at increased risk of developing various cancers, especially of the gastrointestinal and gynaecological tracts. Colonic adenocarcinoma is one of the more common tumours that occur in PJS. We report a young lady presenting with a large ovarian tumour, later diagnosed to have PJS with colonic signet cell adenocarcinoma and synchronous ovarian metastasis.
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spelling pubmed-39209932014-02-12 Krukenberg tumour as the initial presentation of Peutz-Jeghers syndrome Remalayam, Bhavith Kuriakose, Santhosh Kambarath, Prathapan Valiya Mavali, Ramachandran Thazhath Gastroenterol Rep (Oxf) Case Reports Peutz-Jeghers syndrome (PJS) is an hereditary syndrome characterized by gastrointestinal polyposis and mucocutaneous pigmentation. PJS patients are at increased risk of developing various cancers, especially of the gastrointestinal and gynaecological tracts. Colonic adenocarcinoma is one of the more common tumours that occur in PJS. We report a young lady presenting with a large ovarian tumour, later diagnosed to have PJS with colonic signet cell adenocarcinoma and synchronous ovarian metastasis. Oxford University Press 2014-02 2013-12-19 /pmc/articles/PMC3920993/ /pubmed/24760241 http://dx.doi.org/10.1093/gastro/got031 Text en © The Author(s) 2013. Published by Oxford University Press and the Digestive Science Publishing Co. Limited. http://creativecommons.org/licenses/by/3.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/3.0/), which permits unrestricted reuse, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Reports
Remalayam, Bhavith
Kuriakose, Santhosh
Kambarath, Prathapan Valiya
Mavali, Ramachandran Thazhath
Krukenberg tumour as the initial presentation of Peutz-Jeghers syndrome
title Krukenberg tumour as the initial presentation of Peutz-Jeghers syndrome
title_full Krukenberg tumour as the initial presentation of Peutz-Jeghers syndrome
title_fullStr Krukenberg tumour as the initial presentation of Peutz-Jeghers syndrome
title_full_unstemmed Krukenberg tumour as the initial presentation of Peutz-Jeghers syndrome
title_short Krukenberg tumour as the initial presentation of Peutz-Jeghers syndrome
title_sort krukenberg tumour as the initial presentation of peutz-jeghers syndrome
topic Case Reports
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3920993/
https://www.ncbi.nlm.nih.gov/pubmed/24760241
http://dx.doi.org/10.1093/gastro/got031
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