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Epidermolysis bullosa pruriginosa: A report of two cases
Epidermolysis bullosa (EB) pruriginosa is a very rare pattern of dystrophic EB caused by type VII collagen gene mutation, with distinctive clinico-pathological features. It is characterized by nodular prurigo-like lichenified lesions, nail dystrophy, and variable presence of albopapuloid lesions. We...
Autores principales: | , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Medknow Publications & Media Pvt Ltd
2014
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3937487/ https://www.ncbi.nlm.nih.gov/pubmed/24616855 http://dx.doi.org/10.4103/2229-5178.126030 |
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author | Pai, Varadraj Vasant Sori, Tukaram Naveen, Kikkeri Narayanshetty Athanikar, Sharatchandra Bhimrao Rai, Vijetha Shastry, Dinesh Udupi |
author_facet | Pai, Varadraj Vasant Sori, Tukaram Naveen, Kikkeri Narayanshetty Athanikar, Sharatchandra Bhimrao Rai, Vijetha Shastry, Dinesh Udupi |
author_sort | Pai, Varadraj Vasant |
collection | PubMed |
description | Epidermolysis bullosa (EB) pruriginosa is a very rare pattern of dystrophic EB caused by type VII collagen gene mutation, with distinctive clinico-pathological features. It is characterized by nodular prurigo-like lichenified lesions, nail dystrophy, and variable presence of albopapuloid lesions. We report two such cases. |
format | Online Article Text |
id | pubmed-3937487 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2014 |
publisher | Medknow Publications & Media Pvt Ltd |
record_format | MEDLINE/PubMed |
spelling | pubmed-39374872014-03-10 Epidermolysis bullosa pruriginosa: A report of two cases Pai, Varadraj Vasant Sori, Tukaram Naveen, Kikkeri Narayanshetty Athanikar, Sharatchandra Bhimrao Rai, Vijetha Shastry, Dinesh Udupi Indian Dermatol Online J Case Report Epidermolysis bullosa (EB) pruriginosa is a very rare pattern of dystrophic EB caused by type VII collagen gene mutation, with distinctive clinico-pathological features. It is characterized by nodular prurigo-like lichenified lesions, nail dystrophy, and variable presence of albopapuloid lesions. We report two such cases. Medknow Publications & Media Pvt Ltd 2014 /pmc/articles/PMC3937487/ /pubmed/24616855 http://dx.doi.org/10.4103/2229-5178.126030 Text en Copyright: © Indian Dermatology Online Journal http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Pai, Varadraj Vasant Sori, Tukaram Naveen, Kikkeri Narayanshetty Athanikar, Sharatchandra Bhimrao Rai, Vijetha Shastry, Dinesh Udupi Epidermolysis bullosa pruriginosa: A report of two cases |
title | Epidermolysis bullosa pruriginosa: A report of two cases |
title_full | Epidermolysis bullosa pruriginosa: A report of two cases |
title_fullStr | Epidermolysis bullosa pruriginosa: A report of two cases |
title_full_unstemmed | Epidermolysis bullosa pruriginosa: A report of two cases |
title_short | Epidermolysis bullosa pruriginosa: A report of two cases |
title_sort | epidermolysis bullosa pruriginosa: a report of two cases |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3937487/ https://www.ncbi.nlm.nih.gov/pubmed/24616855 http://dx.doi.org/10.4103/2229-5178.126030 |
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