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Epidermolysis bullosa pruriginosa: A report of two cases

Epidermolysis bullosa (EB) pruriginosa is a very rare pattern of dystrophic EB caused by type VII collagen gene mutation, with distinctive clinico-pathological features. It is characterized by nodular prurigo-like lichenified lesions, nail dystrophy, and variable presence of albopapuloid lesions. We...

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Autores principales: Pai, Varadraj Vasant, Sori, Tukaram, Naveen, Kikkeri Narayanshetty, Athanikar, Sharatchandra Bhimrao, Rai, Vijetha, Shastry, Dinesh Udupi
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2014
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3937487/
https://www.ncbi.nlm.nih.gov/pubmed/24616855
http://dx.doi.org/10.4103/2229-5178.126030
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author Pai, Varadraj Vasant
Sori, Tukaram
Naveen, Kikkeri Narayanshetty
Athanikar, Sharatchandra Bhimrao
Rai, Vijetha
Shastry, Dinesh Udupi
author_facet Pai, Varadraj Vasant
Sori, Tukaram
Naveen, Kikkeri Narayanshetty
Athanikar, Sharatchandra Bhimrao
Rai, Vijetha
Shastry, Dinesh Udupi
author_sort Pai, Varadraj Vasant
collection PubMed
description Epidermolysis bullosa (EB) pruriginosa is a very rare pattern of dystrophic EB caused by type VII collagen gene mutation, with distinctive clinico-pathological features. It is characterized by nodular prurigo-like lichenified lesions, nail dystrophy, and variable presence of albopapuloid lesions. We report two such cases.
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spelling pubmed-39374872014-03-10 Epidermolysis bullosa pruriginosa: A report of two cases Pai, Varadraj Vasant Sori, Tukaram Naveen, Kikkeri Narayanshetty Athanikar, Sharatchandra Bhimrao Rai, Vijetha Shastry, Dinesh Udupi Indian Dermatol Online J Case Report Epidermolysis bullosa (EB) pruriginosa is a very rare pattern of dystrophic EB caused by type VII collagen gene mutation, with distinctive clinico-pathological features. It is characterized by nodular prurigo-like lichenified lesions, nail dystrophy, and variable presence of albopapuloid lesions. We report two such cases. Medknow Publications & Media Pvt Ltd 2014 /pmc/articles/PMC3937487/ /pubmed/24616855 http://dx.doi.org/10.4103/2229-5178.126030 Text en Copyright: © Indian Dermatology Online Journal http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Pai, Varadraj Vasant
Sori, Tukaram
Naveen, Kikkeri Narayanshetty
Athanikar, Sharatchandra Bhimrao
Rai, Vijetha
Shastry, Dinesh Udupi
Epidermolysis bullosa pruriginosa: A report of two cases
title Epidermolysis bullosa pruriginosa: A report of two cases
title_full Epidermolysis bullosa pruriginosa: A report of two cases
title_fullStr Epidermolysis bullosa pruriginosa: A report of two cases
title_full_unstemmed Epidermolysis bullosa pruriginosa: A report of two cases
title_short Epidermolysis bullosa pruriginosa: A report of two cases
title_sort epidermolysis bullosa pruriginosa: a report of two cases
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3937487/
https://www.ncbi.nlm.nih.gov/pubmed/24616855
http://dx.doi.org/10.4103/2229-5178.126030
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