Polycystic liver disease presenting as pruritus

Polycystic liver disease (PCLD) is a rare autosomal dominant disorder which usually occurs in association with autosomal dominant polycystic kidney disease. Biliary obstruction is a rare complication of PCLD. Treatment options include percutaneous aspiration and sclerosis, surgical deroofing of cyst...

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Autores principales: Johnson, Deepak Kochummen, Panchili, Shihab, Kolasseri, Sandesh, Mavali, Ramachandran Thazhath
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hellenic Society of Gastroenterology 2014
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3959546/
https://www.ncbi.nlm.nih.gov/pubmed/24714704
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author Johnson, Deepak Kochummen
Panchili, Shihab
Kolasseri, Sandesh
Mavali, Ramachandran Thazhath
author_facet Johnson, Deepak Kochummen
Panchili, Shihab
Kolasseri, Sandesh
Mavali, Ramachandran Thazhath
author_sort Johnson, Deepak Kochummen
collection PubMed
description Polycystic liver disease (PCLD) is a rare autosomal dominant disorder which usually occurs in association with autosomal dominant polycystic kidney disease. Biliary obstruction is a rare complication of PCLD. Treatment options include percutaneous aspiration and sclerosis, surgical deroofing of cysts, liver resection or liver transplantation. Medical treatment involves the use of somatostatin analogues or mTOR inhibitors. We present a case of PCLD presenting for the first time with longstanding pruritus as the only symptom.
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spelling pubmed-39595462014-04-07 Polycystic liver disease presenting as pruritus Johnson, Deepak Kochummen Panchili, Shihab Kolasseri, Sandesh Mavali, Ramachandran Thazhath Ann Gastroenterol Case Report Polycystic liver disease (PCLD) is a rare autosomal dominant disorder which usually occurs in association with autosomal dominant polycystic kidney disease. Biliary obstruction is a rare complication of PCLD. Treatment options include percutaneous aspiration and sclerosis, surgical deroofing of cysts, liver resection or liver transplantation. Medical treatment involves the use of somatostatin analogues or mTOR inhibitors. We present a case of PCLD presenting for the first time with longstanding pruritus as the only symptom. Hellenic Society of Gastroenterology 2014 /pmc/articles/PMC3959546/ /pubmed/24714704 Text en Copyright: © Hellenic Society of Gastroenterology http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Johnson, Deepak Kochummen
Panchili, Shihab
Kolasseri, Sandesh
Mavali, Ramachandran Thazhath
Polycystic liver disease presenting as pruritus
title Polycystic liver disease presenting as pruritus
title_full Polycystic liver disease presenting as pruritus
title_fullStr Polycystic liver disease presenting as pruritus
title_full_unstemmed Polycystic liver disease presenting as pruritus
title_short Polycystic liver disease presenting as pruritus
title_sort polycystic liver disease presenting as pruritus
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3959546/
https://www.ncbi.nlm.nih.gov/pubmed/24714704
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AT kolasserisandesh polycysticliverdiseasepresentingaspruritus
AT mavaliramachandranthazhath polycysticliverdiseasepresentingaspruritus

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