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Oral rhabdomyosarcoma-embryonal subtype in an adult: A rarity

Rhabdomyosarcoma is a malignant tumor composed of neoplastic mesenchymal cells, with varying degrees of striated muscle cell differentiation. With most cases occurring in children younger than 10 years, it is remarkably rare in adults. Further in adults, the typical pediatric rhabdomyosarcoma varian...

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Autores principales: Arul, A. Sri Kennath J., Verma, Sonika, Arul, A. Sri Sennath J., Verma, Rashmika
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2014
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3961943/
https://www.ncbi.nlm.nih.gov/pubmed/24678235
http://dx.doi.org/10.4103/0976-9668.127347
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author Arul, A. Sri Kennath J.
Verma, Sonika
Arul, A. Sri Sennath J.
Verma, Rashmika
author_facet Arul, A. Sri Kennath J.
Verma, Sonika
Arul, A. Sri Sennath J.
Verma, Rashmika
author_sort Arul, A. Sri Kennath J.
collection PubMed
description Rhabdomyosarcoma is a malignant tumor composed of neoplastic mesenchymal cells, with varying degrees of striated muscle cell differentiation. With most cases occurring in children younger than 10 years, it is remarkably rare in adults. Further in adults, the typical pediatric rhabdomyosarcoma variants (embryonal and alveolar sub-types) occur less frequently and exhibit predilection for viscera followed by the head and neck region. A rare case of embryonal rhabdomyosarcoma arising from the buccal mucosa in a 36-year old male patient is herewith reported. Recognition of the correct diagnosis and histological sub-type is of critical importance in the therapy of this disease, since the treatment is not uniform in the literature because of the rarity of this neoplasm in the adult population.
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spelling pubmed-39619432014-03-27 Oral rhabdomyosarcoma-embryonal subtype in an adult: A rarity Arul, A. Sri Kennath J. Verma, Sonika Arul, A. Sri Sennath J. Verma, Rashmika J Nat Sci Biol Med Case Report Rhabdomyosarcoma is a malignant tumor composed of neoplastic mesenchymal cells, with varying degrees of striated muscle cell differentiation. With most cases occurring in children younger than 10 years, it is remarkably rare in adults. Further in adults, the typical pediatric rhabdomyosarcoma variants (embryonal and alveolar sub-types) occur less frequently and exhibit predilection for viscera followed by the head and neck region. A rare case of embryonal rhabdomyosarcoma arising from the buccal mucosa in a 36-year old male patient is herewith reported. Recognition of the correct diagnosis and histological sub-type is of critical importance in the therapy of this disease, since the treatment is not uniform in the literature because of the rarity of this neoplasm in the adult population. Medknow Publications & Media Pvt Ltd 2014 /pmc/articles/PMC3961943/ /pubmed/24678235 http://dx.doi.org/10.4103/0976-9668.127347 Text en Copyright: © Journal of Natural Science, Biology and Medicine http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Arul, A. Sri Kennath J.
Verma, Sonika
Arul, A. Sri Sennath J.
Verma, Rashmika
Oral rhabdomyosarcoma-embryonal subtype in an adult: A rarity
title Oral rhabdomyosarcoma-embryonal subtype in an adult: A rarity
title_full Oral rhabdomyosarcoma-embryonal subtype in an adult: A rarity
title_fullStr Oral rhabdomyosarcoma-embryonal subtype in an adult: A rarity
title_full_unstemmed Oral rhabdomyosarcoma-embryonal subtype in an adult: A rarity
title_short Oral rhabdomyosarcoma-embryonal subtype in an adult: A rarity
title_sort oral rhabdomyosarcoma-embryonal subtype in an adult: a rarity
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3961943/
https://www.ncbi.nlm.nih.gov/pubmed/24678235
http://dx.doi.org/10.4103/0976-9668.127347
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