Cargando…
Oral rhabdomyosarcoma-embryonal subtype in an adult: A rarity
Rhabdomyosarcoma is a malignant tumor composed of neoplastic mesenchymal cells, with varying degrees of striated muscle cell differentiation. With most cases occurring in children younger than 10 years, it is remarkably rare in adults. Further in adults, the typical pediatric rhabdomyosarcoma varian...
Autores principales: | , , , |
---|---|
Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Medknow Publications & Media Pvt Ltd
2014
|
Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3961943/ https://www.ncbi.nlm.nih.gov/pubmed/24678235 http://dx.doi.org/10.4103/0976-9668.127347 |
_version_ | 1782308367204614144 |
---|---|
author | Arul, A. Sri Kennath J. Verma, Sonika Arul, A. Sri Sennath J. Verma, Rashmika |
author_facet | Arul, A. Sri Kennath J. Verma, Sonika Arul, A. Sri Sennath J. Verma, Rashmika |
author_sort | Arul, A. Sri Kennath J. |
collection | PubMed |
description | Rhabdomyosarcoma is a malignant tumor composed of neoplastic mesenchymal cells, with varying degrees of striated muscle cell differentiation. With most cases occurring in children younger than 10 years, it is remarkably rare in adults. Further in adults, the typical pediatric rhabdomyosarcoma variants (embryonal and alveolar sub-types) occur less frequently and exhibit predilection for viscera followed by the head and neck region. A rare case of embryonal rhabdomyosarcoma arising from the buccal mucosa in a 36-year old male patient is herewith reported. Recognition of the correct diagnosis and histological sub-type is of critical importance in the therapy of this disease, since the treatment is not uniform in the literature because of the rarity of this neoplasm in the adult population. |
format | Online Article Text |
id | pubmed-3961943 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2014 |
publisher | Medknow Publications & Media Pvt Ltd |
record_format | MEDLINE/PubMed |
spelling | pubmed-39619432014-03-27 Oral rhabdomyosarcoma-embryonal subtype in an adult: A rarity Arul, A. Sri Kennath J. Verma, Sonika Arul, A. Sri Sennath J. Verma, Rashmika J Nat Sci Biol Med Case Report Rhabdomyosarcoma is a malignant tumor composed of neoplastic mesenchymal cells, with varying degrees of striated muscle cell differentiation. With most cases occurring in children younger than 10 years, it is remarkably rare in adults. Further in adults, the typical pediatric rhabdomyosarcoma variants (embryonal and alveolar sub-types) occur less frequently and exhibit predilection for viscera followed by the head and neck region. A rare case of embryonal rhabdomyosarcoma arising from the buccal mucosa in a 36-year old male patient is herewith reported. Recognition of the correct diagnosis and histological sub-type is of critical importance in the therapy of this disease, since the treatment is not uniform in the literature because of the rarity of this neoplasm in the adult population. Medknow Publications & Media Pvt Ltd 2014 /pmc/articles/PMC3961943/ /pubmed/24678235 http://dx.doi.org/10.4103/0976-9668.127347 Text en Copyright: © Journal of Natural Science, Biology and Medicine http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Arul, A. Sri Kennath J. Verma, Sonika Arul, A. Sri Sennath J. Verma, Rashmika Oral rhabdomyosarcoma-embryonal subtype in an adult: A rarity |
title | Oral rhabdomyosarcoma-embryonal subtype in an adult: A rarity |
title_full | Oral rhabdomyosarcoma-embryonal subtype in an adult: A rarity |
title_fullStr | Oral rhabdomyosarcoma-embryonal subtype in an adult: A rarity |
title_full_unstemmed | Oral rhabdomyosarcoma-embryonal subtype in an adult: A rarity |
title_short | Oral rhabdomyosarcoma-embryonal subtype in an adult: A rarity |
title_sort | oral rhabdomyosarcoma-embryonal subtype in an adult: a rarity |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3961943/ https://www.ncbi.nlm.nih.gov/pubmed/24678235 http://dx.doi.org/10.4103/0976-9668.127347 |
work_keys_str_mv | AT arulasrikennathj oralrhabdomyosarcomaembryonalsubtypeinanadultararity AT vermasonika oralrhabdomyosarcomaembryonalsubtypeinanadultararity AT arulasrisennathj oralrhabdomyosarcomaembryonalsubtypeinanadultararity AT vermarashmika oralrhabdomyosarcomaembryonalsubtypeinanadultararity |