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Superior mediastinal paraganglioma associated with von Hippel-Lindau syndrome: report of a case

Extra-adrenal pheochromocytomas are termed paragangliomas. Paragangliomas in the mediastinum, especially the superior mediastinum, are extremely rare. It is known that paragangliomas or pheochromocytomas occur in combination with von Hippel-Lindau syndrome. We present the case of a non-functional su...

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Detalles Bibliográficos
Autores principales: Takahashi, Tsuyoshi, Nogimura, Hiroshi, Kuriki, Ken, Kobayashi, Ryo
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2014
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3977687/
https://www.ncbi.nlm.nih.gov/pubmed/24678933
http://dx.doi.org/10.1186/1477-7819-12-74
Descripción
Sumario:Extra-adrenal pheochromocytomas are termed paragangliomas. Paragangliomas in the mediastinum, especially the superior mediastinum, are extremely rare. It is known that paragangliomas or pheochromocytomas occur in combination with von Hippel-Lindau syndrome. We present the case of a non-functional superior mediastinal paraganglioma in a patient with von Hippel-Lindau syndrome, without a familial history suggestive of the condition. This case highlights that we should be aware of possible sporadic von Hippel-Lindau syndrome in patients with a mediastinal paraganglioma.