A rare case of primary cutaneous follicle centre lymphoma presenting as a giant tumour of the scalp and combined with JAK2V617F positive essential thrombocythaemia

Primary cutaneous follicle centre lymphoma (PCFCL) is a rare cutaneous B cell lymphoma in middle-age adults with excellent prognosis. Here we present a case of a patient with a PCFCL in the form of a giant tumour of the scalp in combination with a myeloproliferative neoplasm, JAK2V617F positive esse...

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Detalles Bibliográficos
Autores principales: Tirefort, Yordanka, Pham, Xuan-Cuong, Ibrahim, Yasmine Lucile, Lecompte, Thomas Pierre, Matthes, Thomas, Prins, Christa, Cortes, Begonia, Bernimoulin, Michael, Chalandon, Yves, Samii, Kaveh
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2014
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3978001/
https://www.ncbi.nlm.nih.gov/pubmed/24690328
http://dx.doi.org/10.1186/2050-7771-2-7
Descripción
Sumario:Primary cutaneous follicle centre lymphoma (PCFCL) is a rare cutaneous B cell lymphoma in middle-age adults with excellent prognosis. Here we present a case of a patient with a PCFCL in the form of a giant tumour of the scalp in combination with a myeloproliferative neoplasm, JAK2V617F positive essential thrombocythaemia. This case may be of interest because of the favourable outcome in spite of the large size of the PCFCL, the rare combination with essential thrombocythaemia and because it contributes to discussion on the role of JAK2 mutation in such patients.

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