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A rare case of primary cutaneous follicle centre lymphoma presenting as a giant tumour of the scalp and combined with JAK2V617F positive essential thrombocythaemia

Primary cutaneous follicle centre lymphoma (PCFCL) is a rare cutaneous B cell lymphoma in middle-age adults with excellent prognosis. Here we present a case of a patient with a PCFCL in the form of a giant tumour of the scalp in combination with a myeloproliferative neoplasm, JAK2V617F positive esse...

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Autores principales: Tirefort, Yordanka, Pham, Xuan-Cuong, Ibrahim, Yasmine Lucile, Lecompte, Thomas Pierre, Matthes, Thomas, Prins, Christa, Cortes, Begonia, Bernimoulin, Michael, Chalandon, Yves, Samii, Kaveh
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2014
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3978001/
https://www.ncbi.nlm.nih.gov/pubmed/24690328
http://dx.doi.org/10.1186/2050-7771-2-7
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author Tirefort, Yordanka
Pham, Xuan-Cuong
Ibrahim, Yasmine Lucile
Lecompte, Thomas Pierre
Matthes, Thomas
Prins, Christa
Cortes, Begonia
Bernimoulin, Michael
Chalandon, Yves
Samii, Kaveh
author_facet Tirefort, Yordanka
Pham, Xuan-Cuong
Ibrahim, Yasmine Lucile
Lecompte, Thomas Pierre
Matthes, Thomas
Prins, Christa
Cortes, Begonia
Bernimoulin, Michael
Chalandon, Yves
Samii, Kaveh
author_sort Tirefort, Yordanka
collection PubMed
description Primary cutaneous follicle centre lymphoma (PCFCL) is a rare cutaneous B cell lymphoma in middle-age adults with excellent prognosis. Here we present a case of a patient with a PCFCL in the form of a giant tumour of the scalp in combination with a myeloproliferative neoplasm, JAK2V617F positive essential thrombocythaemia. This case may be of interest because of the favourable outcome in spite of the large size of the PCFCL, the rare combination with essential thrombocythaemia and because it contributes to discussion on the role of JAK2 mutation in such patients.
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spelling pubmed-39780012014-04-08 A rare case of primary cutaneous follicle centre lymphoma presenting as a giant tumour of the scalp and combined with JAK2V617F positive essential thrombocythaemia Tirefort, Yordanka Pham, Xuan-Cuong Ibrahim, Yasmine Lucile Lecompte, Thomas Pierre Matthes, Thomas Prins, Christa Cortes, Begonia Bernimoulin, Michael Chalandon, Yves Samii, Kaveh Biomark Res Case Report Primary cutaneous follicle centre lymphoma (PCFCL) is a rare cutaneous B cell lymphoma in middle-age adults with excellent prognosis. Here we present a case of a patient with a PCFCL in the form of a giant tumour of the scalp in combination with a myeloproliferative neoplasm, JAK2V617F positive essential thrombocythaemia. This case may be of interest because of the favourable outcome in spite of the large size of the PCFCL, the rare combination with essential thrombocythaemia and because it contributes to discussion on the role of JAK2 mutation in such patients. BioMed Central 2014-04-01 /pmc/articles/PMC3978001/ /pubmed/24690328 http://dx.doi.org/10.1186/2050-7771-2-7 Text en Copyright © 2014 Tirefort et al.; licensee BioMed Central Ltd. http://creativecommons.org/licenses/by/2.0 This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/2.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly credited. The Creative Commons Public Domain Dedication waiver (http://creativecommons.org/publicdomain/zero/1.0/) applies to the data made available in this article, unless otherwise stated.
spellingShingle Case Report
Tirefort, Yordanka
Pham, Xuan-Cuong
Ibrahim, Yasmine Lucile
Lecompte, Thomas Pierre
Matthes, Thomas
Prins, Christa
Cortes, Begonia
Bernimoulin, Michael
Chalandon, Yves
Samii, Kaveh
A rare case of primary cutaneous follicle centre lymphoma presenting as a giant tumour of the scalp and combined with JAK2V617F positive essential thrombocythaemia
title A rare case of primary cutaneous follicle centre lymphoma presenting as a giant tumour of the scalp and combined with JAK2V617F positive essential thrombocythaemia
title_full A rare case of primary cutaneous follicle centre lymphoma presenting as a giant tumour of the scalp and combined with JAK2V617F positive essential thrombocythaemia
title_fullStr A rare case of primary cutaneous follicle centre lymphoma presenting as a giant tumour of the scalp and combined with JAK2V617F positive essential thrombocythaemia
title_full_unstemmed A rare case of primary cutaneous follicle centre lymphoma presenting as a giant tumour of the scalp and combined with JAK2V617F positive essential thrombocythaemia
title_short A rare case of primary cutaneous follicle centre lymphoma presenting as a giant tumour of the scalp and combined with JAK2V617F positive essential thrombocythaemia
title_sort rare case of primary cutaneous follicle centre lymphoma presenting as a giant tumour of the scalp and combined with jak2v617f positive essential thrombocythaemia
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3978001/
https://www.ncbi.nlm.nih.gov/pubmed/24690328
http://dx.doi.org/10.1186/2050-7771-2-7
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