Cargando…
A rare case of primary cutaneous follicle centre lymphoma presenting as a giant tumour of the scalp and combined with JAK2V617F positive essential thrombocythaemia
Primary cutaneous follicle centre lymphoma (PCFCL) is a rare cutaneous B cell lymphoma in middle-age adults with excellent prognosis. Here we present a case of a patient with a PCFCL in the form of a giant tumour of the scalp in combination with a myeloproliferative neoplasm, JAK2V617F positive esse...
Autores principales: | , , , , , , , , , |
---|---|
Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
BioMed Central
2014
|
Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3978001/ https://www.ncbi.nlm.nih.gov/pubmed/24690328 http://dx.doi.org/10.1186/2050-7771-2-7 |
_version_ | 1782310493503881216 |
---|---|
author | Tirefort, Yordanka Pham, Xuan-Cuong Ibrahim, Yasmine Lucile Lecompte, Thomas Pierre Matthes, Thomas Prins, Christa Cortes, Begonia Bernimoulin, Michael Chalandon, Yves Samii, Kaveh |
author_facet | Tirefort, Yordanka Pham, Xuan-Cuong Ibrahim, Yasmine Lucile Lecompte, Thomas Pierre Matthes, Thomas Prins, Christa Cortes, Begonia Bernimoulin, Michael Chalandon, Yves Samii, Kaveh |
author_sort | Tirefort, Yordanka |
collection | PubMed |
description | Primary cutaneous follicle centre lymphoma (PCFCL) is a rare cutaneous B cell lymphoma in middle-age adults with excellent prognosis. Here we present a case of a patient with a PCFCL in the form of a giant tumour of the scalp in combination with a myeloproliferative neoplasm, JAK2V617F positive essential thrombocythaemia. This case may be of interest because of the favourable outcome in spite of the large size of the PCFCL, the rare combination with essential thrombocythaemia and because it contributes to discussion on the role of JAK2 mutation in such patients. |
format | Online Article Text |
id | pubmed-3978001 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2014 |
publisher | BioMed Central |
record_format | MEDLINE/PubMed |
spelling | pubmed-39780012014-04-08 A rare case of primary cutaneous follicle centre lymphoma presenting as a giant tumour of the scalp and combined with JAK2V617F positive essential thrombocythaemia Tirefort, Yordanka Pham, Xuan-Cuong Ibrahim, Yasmine Lucile Lecompte, Thomas Pierre Matthes, Thomas Prins, Christa Cortes, Begonia Bernimoulin, Michael Chalandon, Yves Samii, Kaveh Biomark Res Case Report Primary cutaneous follicle centre lymphoma (PCFCL) is a rare cutaneous B cell lymphoma in middle-age adults with excellent prognosis. Here we present a case of a patient with a PCFCL in the form of a giant tumour of the scalp in combination with a myeloproliferative neoplasm, JAK2V617F positive essential thrombocythaemia. This case may be of interest because of the favourable outcome in spite of the large size of the PCFCL, the rare combination with essential thrombocythaemia and because it contributes to discussion on the role of JAK2 mutation in such patients. BioMed Central 2014-04-01 /pmc/articles/PMC3978001/ /pubmed/24690328 http://dx.doi.org/10.1186/2050-7771-2-7 Text en Copyright © 2014 Tirefort et al.; licensee BioMed Central Ltd. http://creativecommons.org/licenses/by/2.0 This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/2.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly credited. The Creative Commons Public Domain Dedication waiver (http://creativecommons.org/publicdomain/zero/1.0/) applies to the data made available in this article, unless otherwise stated. |
spellingShingle | Case Report Tirefort, Yordanka Pham, Xuan-Cuong Ibrahim, Yasmine Lucile Lecompte, Thomas Pierre Matthes, Thomas Prins, Christa Cortes, Begonia Bernimoulin, Michael Chalandon, Yves Samii, Kaveh A rare case of primary cutaneous follicle centre lymphoma presenting as a giant tumour of the scalp and combined with JAK2V617F positive essential thrombocythaemia |
title | A rare case of primary cutaneous follicle centre lymphoma presenting as a giant tumour of the scalp and combined with JAK2V617F positive essential thrombocythaemia |
title_full | A rare case of primary cutaneous follicle centre lymphoma presenting as a giant tumour of the scalp and combined with JAK2V617F positive essential thrombocythaemia |
title_fullStr | A rare case of primary cutaneous follicle centre lymphoma presenting as a giant tumour of the scalp and combined with JAK2V617F positive essential thrombocythaemia |
title_full_unstemmed | A rare case of primary cutaneous follicle centre lymphoma presenting as a giant tumour of the scalp and combined with JAK2V617F positive essential thrombocythaemia |
title_short | A rare case of primary cutaneous follicle centre lymphoma presenting as a giant tumour of the scalp and combined with JAK2V617F positive essential thrombocythaemia |
title_sort | rare case of primary cutaneous follicle centre lymphoma presenting as a giant tumour of the scalp and combined with jak2v617f positive essential thrombocythaemia |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3978001/ https://www.ncbi.nlm.nih.gov/pubmed/24690328 http://dx.doi.org/10.1186/2050-7771-2-7 |
work_keys_str_mv | AT tirefortyordanka ararecaseofprimarycutaneousfolliclecentrelymphomapresentingasagianttumourofthescalpandcombinedwithjak2v617fpositiveessentialthrombocythaemia AT phamxuancuong ararecaseofprimarycutaneousfolliclecentrelymphomapresentingasagianttumourofthescalpandcombinedwithjak2v617fpositiveessentialthrombocythaemia AT ibrahimyasminelucile ararecaseofprimarycutaneousfolliclecentrelymphomapresentingasagianttumourofthescalpandcombinedwithjak2v617fpositiveessentialthrombocythaemia AT lecomptethomaspierre ararecaseofprimarycutaneousfolliclecentrelymphomapresentingasagianttumourofthescalpandcombinedwithjak2v617fpositiveessentialthrombocythaemia AT matthesthomas ararecaseofprimarycutaneousfolliclecentrelymphomapresentingasagianttumourofthescalpandcombinedwithjak2v617fpositiveessentialthrombocythaemia AT prinschrista ararecaseofprimarycutaneousfolliclecentrelymphomapresentingasagianttumourofthescalpandcombinedwithjak2v617fpositiveessentialthrombocythaemia AT cortesbegonia ararecaseofprimarycutaneousfolliclecentrelymphomapresentingasagianttumourofthescalpandcombinedwithjak2v617fpositiveessentialthrombocythaemia AT bernimoulinmichael ararecaseofprimarycutaneousfolliclecentrelymphomapresentingasagianttumourofthescalpandcombinedwithjak2v617fpositiveessentialthrombocythaemia AT chalandonyves ararecaseofprimarycutaneousfolliclecentrelymphomapresentingasagianttumourofthescalpandcombinedwithjak2v617fpositiveessentialthrombocythaemia AT samiikaveh ararecaseofprimarycutaneousfolliclecentrelymphomapresentingasagianttumourofthescalpandcombinedwithjak2v617fpositiveessentialthrombocythaemia AT tirefortyordanka rarecaseofprimarycutaneousfolliclecentrelymphomapresentingasagianttumourofthescalpandcombinedwithjak2v617fpositiveessentialthrombocythaemia AT phamxuancuong rarecaseofprimarycutaneousfolliclecentrelymphomapresentingasagianttumourofthescalpandcombinedwithjak2v617fpositiveessentialthrombocythaemia AT ibrahimyasminelucile rarecaseofprimarycutaneousfolliclecentrelymphomapresentingasagianttumourofthescalpandcombinedwithjak2v617fpositiveessentialthrombocythaemia AT lecomptethomaspierre rarecaseofprimarycutaneousfolliclecentrelymphomapresentingasagianttumourofthescalpandcombinedwithjak2v617fpositiveessentialthrombocythaemia AT matthesthomas rarecaseofprimarycutaneousfolliclecentrelymphomapresentingasagianttumourofthescalpandcombinedwithjak2v617fpositiveessentialthrombocythaemia AT prinschrista rarecaseofprimarycutaneousfolliclecentrelymphomapresentingasagianttumourofthescalpandcombinedwithjak2v617fpositiveessentialthrombocythaemia AT cortesbegonia rarecaseofprimarycutaneousfolliclecentrelymphomapresentingasagianttumourofthescalpandcombinedwithjak2v617fpositiveessentialthrombocythaemia AT bernimoulinmichael rarecaseofprimarycutaneousfolliclecentrelymphomapresentingasagianttumourofthescalpandcombinedwithjak2v617fpositiveessentialthrombocythaemia AT chalandonyves rarecaseofprimarycutaneousfolliclecentrelymphomapresentingasagianttumourofthescalpandcombinedwithjak2v617fpositiveessentialthrombocythaemia AT samiikaveh rarecaseofprimarycutaneousfolliclecentrelymphomapresentingasagianttumourofthescalpandcombinedwithjak2v617fpositiveessentialthrombocythaemia |