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Hepatobiliary rhabdomyosarcoma mimicking choledochal cyst: Lessons learned()
INTRODUCTION: The differential diagnosis of hepatic cystic lesions is a challenging process especially in case of hepatic rhabdomyosarcoma (HRMS) presenting as hepatic cyst. PRESENTATION OF CASE: We introduce our experience with a case of HRMS in a 3-year-old female patient who was misdiagnosed to h...
Autores principales: | , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Elsevier
2014
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3980419/ https://www.ncbi.nlm.nih.gov/pubmed/24636980 http://dx.doi.org/10.1016/j.ijscr.2014.01.020 |
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author | Elwahab, Mohamed Abd Hamed, Hosam Shehta, Ahmed Ali, Mahmoud Zalata, Khaled |
author_facet | Elwahab, Mohamed Abd Hamed, Hosam Shehta, Ahmed Ali, Mahmoud Zalata, Khaled |
author_sort | Elwahab, Mohamed Abd |
collection | PubMed |
description | INTRODUCTION: The differential diagnosis of hepatic cystic lesions is a challenging process especially in case of hepatic rhabdomyosarcoma (HRMS) presenting as hepatic cyst. PRESENTATION OF CASE: We introduce our experience with a case of HRMS in a 3-year-old female patient who was misdiagnosed to have type IV-A choledochal cyst and definitive correct diagnosis was reached after the pathological and immunohistochemical examination of the surgically resected lesion. This case presentation is followed by important practical messages to hepatobiliary surgeons regarding HRMS. DISCUSSION: HRMS is a rare pediatric tumor. Jaundice is the most common presentation of HRMS followed by abdominal pain and vomiting. Great effort is needed to differentiate the tumor from choledochal cyst and infectious hepatitis. Through evaluation using available imaging studies together with clinical anticipation is mandatory for establishing the correct diagnosis. CONCLUSION: Differentiation of HRMs from choledochal cyst mandates through evaluation and clinical anticipation. HRMS should be suspected in any child with obstructive jaundice. Once diagnosis is established, multidisciplinary treatment is the best management strategy and it has proved better surgical outcome and long term survival. |
format | Online Article Text |
id | pubmed-3980419 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2014 |
publisher | Elsevier |
record_format | MEDLINE/PubMed |
spelling | pubmed-39804192014-04-10 Hepatobiliary rhabdomyosarcoma mimicking choledochal cyst: Lessons learned() Elwahab, Mohamed Abd Hamed, Hosam Shehta, Ahmed Ali, Mahmoud Zalata, Khaled Int J Surg Case Rep Article INTRODUCTION: The differential diagnosis of hepatic cystic lesions is a challenging process especially in case of hepatic rhabdomyosarcoma (HRMS) presenting as hepatic cyst. PRESENTATION OF CASE: We introduce our experience with a case of HRMS in a 3-year-old female patient who was misdiagnosed to have type IV-A choledochal cyst and definitive correct diagnosis was reached after the pathological and immunohistochemical examination of the surgically resected lesion. This case presentation is followed by important practical messages to hepatobiliary surgeons regarding HRMS. DISCUSSION: HRMS is a rare pediatric tumor. Jaundice is the most common presentation of HRMS followed by abdominal pain and vomiting. Great effort is needed to differentiate the tumor from choledochal cyst and infectious hepatitis. Through evaluation using available imaging studies together with clinical anticipation is mandatory for establishing the correct diagnosis. CONCLUSION: Differentiation of HRMs from choledochal cyst mandates through evaluation and clinical anticipation. HRMS should be suspected in any child with obstructive jaundice. Once diagnosis is established, multidisciplinary treatment is the best management strategy and it has proved better surgical outcome and long term survival. Elsevier 2014-02-07 /pmc/articles/PMC3980419/ /pubmed/24636980 http://dx.doi.org/10.1016/j.ijscr.2014.01.020 Text en © 2014 The Authors http://creativecommons.org/licenses/by-nc-nd/3.0/ This is an open-access article distributed under the terms of the Creative Commons Attribution-NonCommercial-No Derivative Works License, which permits non-commercial use, distribution, and reproduction in any medium, provided the original author and source are credited. |
spellingShingle | Article Elwahab, Mohamed Abd Hamed, Hosam Shehta, Ahmed Ali, Mahmoud Zalata, Khaled Hepatobiliary rhabdomyosarcoma mimicking choledochal cyst: Lessons learned() |
title | Hepatobiliary rhabdomyosarcoma mimicking choledochal cyst: Lessons learned() |
title_full | Hepatobiliary rhabdomyosarcoma mimicking choledochal cyst: Lessons learned() |
title_fullStr | Hepatobiliary rhabdomyosarcoma mimicking choledochal cyst: Lessons learned() |
title_full_unstemmed | Hepatobiliary rhabdomyosarcoma mimicking choledochal cyst: Lessons learned() |
title_short | Hepatobiliary rhabdomyosarcoma mimicking choledochal cyst: Lessons learned() |
title_sort | hepatobiliary rhabdomyosarcoma mimicking choledochal cyst: lessons learned() |
topic | Article |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3980419/ https://www.ncbi.nlm.nih.gov/pubmed/24636980 http://dx.doi.org/10.1016/j.ijscr.2014.01.020 |
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