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Poland's Syndrome with Absent Limb Anomalies
Poland's syndrome comprises a spectrum of chest-wall deformities affecting, to various degrees, the rib cage, the chest-wall muscles, neurovascular structures of the ipsilateral arm and the overlying breast. We present a neonate with features of depressed right chest-wall with no respiratory di...
Autores principales: | , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Medknow Publications & Media Pvt Ltd
2014
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3982340/ https://www.ncbi.nlm.nih.gov/pubmed/24741541 http://dx.doi.org/10.4103/2249-4847.128735 |
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author | Al Faleh, Khalid Al Saadi, Muslim Khalid-Bantuas, Shialinee |
author_facet | Al Faleh, Khalid Al Saadi, Muslim Khalid-Bantuas, Shialinee |
author_sort | Al Faleh, Khalid |
collection | PubMed |
description | Poland's syndrome comprises a spectrum of chest-wall deformities affecting, to various degrees, the rib cage, the chest-wall muscles, neurovascular structures of the ipsilateral arm and the overlying breast. We present a neonate with features of depressed right chest-wall with no respiratory distress. Computed tomography showed hypolasia of the right pectoralis major muscle, with reduced subcutaneous fat on the ipsilateral side of the chest, with abnormalities of the ribs on the same side but absent upper limb deformities. There is negative history of other family members of being affected. |
format | Online Article Text |
id | pubmed-3982340 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2014 |
publisher | Medknow Publications & Media Pvt Ltd |
record_format | MEDLINE/PubMed |
spelling | pubmed-39823402014-04-16 Poland's Syndrome with Absent Limb Anomalies Al Faleh, Khalid Al Saadi, Muslim Khalid-Bantuas, Shialinee J Clin Neonatol Case Report Poland's syndrome comprises a spectrum of chest-wall deformities affecting, to various degrees, the rib cage, the chest-wall muscles, neurovascular structures of the ipsilateral arm and the overlying breast. We present a neonate with features of depressed right chest-wall with no respiratory distress. Computed tomography showed hypolasia of the right pectoralis major muscle, with reduced subcutaneous fat on the ipsilateral side of the chest, with abnormalities of the ribs on the same side but absent upper limb deformities. There is negative history of other family members of being affected. Medknow Publications & Media Pvt Ltd 2014 /pmc/articles/PMC3982340/ /pubmed/24741541 http://dx.doi.org/10.4103/2249-4847.128735 Text en Copyright: © Journal of Clinical Neonatology http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Al Faleh, Khalid Al Saadi, Muslim Khalid-Bantuas, Shialinee Poland's Syndrome with Absent Limb Anomalies |
title | Poland's Syndrome with Absent Limb Anomalies |
title_full | Poland's Syndrome with Absent Limb Anomalies |
title_fullStr | Poland's Syndrome with Absent Limb Anomalies |
title_full_unstemmed | Poland's Syndrome with Absent Limb Anomalies |
title_short | Poland's Syndrome with Absent Limb Anomalies |
title_sort | poland's syndrome with absent limb anomalies |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3982340/ https://www.ncbi.nlm.nih.gov/pubmed/24741541 http://dx.doi.org/10.4103/2249-4847.128735 |
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