Pneumonectomy Case in a Newborn with Congenital Pulmonary Lymphangiectasia

Congenital pulmonary lymphangiectasia (CPL) is a rare lymphatic pulmonary abnormality. CPL with respiratory distress has a poor prognosis, and is frequently fatal in neonates. We report a case of pneumonectomy for CPL in a newborn. An infant girl, born at 39 weeks' after an uncomplicated pregna...

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Autores principales: Hwang, Joon Ho, Kim, Joo Heon, Hwang, Jung Ju, Kim, Kyu Soon, Kim, Seung Yeon
Formato: Online Artículo Texto
Lenguaje:English
Publicado: The Korean Academy of Medical Sciences 2014
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3991809/
https://www.ncbi.nlm.nih.gov/pubmed/24753713
http://dx.doi.org/10.3346/jkms.2014.29.4.609
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author Hwang, Joon Ho
Kim, Joo Heon
Hwang, Jung Ju
Kim, Kyu Soon
Kim, Seung Yeon
author_facet Hwang, Joon Ho
Kim, Joo Heon
Hwang, Jung Ju
Kim, Kyu Soon
Kim, Seung Yeon
author_sort Hwang, Joon Ho
collection PubMed
description Congenital pulmonary lymphangiectasia (CPL) is a rare lymphatic pulmonary abnormality. CPL with respiratory distress has a poor prognosis, and is frequently fatal in neonates. We report a case of pneumonectomy for CPL in a newborn. An infant girl, born at 39 weeks' after an uncomplicated pregnancy, exhibited respiratory distress 1 hr after birth, which necessitated intubation and aggressive ventilator care. Right pneumonectomy was performed after her symptoms worsened. Histologic examination indicated CPL. She is currently 12 months old and developing normally. Pneumonectomy can be considered for treating respiratory symptoms for improving chances of survival in cases with unilateral CPL. GRAPHICAL ABSTRACT: [Image: see text]
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spelling pubmed-39918092014-04-21 Pneumonectomy Case in a Newborn with Congenital Pulmonary Lymphangiectasia Hwang, Joon Ho Kim, Joo Heon Hwang, Jung Ju Kim, Kyu Soon Kim, Seung Yeon J Korean Med Sci Case Report Congenital pulmonary lymphangiectasia (CPL) is a rare lymphatic pulmonary abnormality. CPL with respiratory distress has a poor prognosis, and is frequently fatal in neonates. We report a case of pneumonectomy for CPL in a newborn. An infant girl, born at 39 weeks' after an uncomplicated pregnancy, exhibited respiratory distress 1 hr after birth, which necessitated intubation and aggressive ventilator care. Right pneumonectomy was performed after her symptoms worsened. Histologic examination indicated CPL. She is currently 12 months old and developing normally. Pneumonectomy can be considered for treating respiratory symptoms for improving chances of survival in cases with unilateral CPL. GRAPHICAL ABSTRACT: [Image: see text] The Korean Academy of Medical Sciences 2014-04 2014-04-01 /pmc/articles/PMC3991809/ /pubmed/24753713 http://dx.doi.org/10.3346/jkms.2014.29.4.609 Text en © 2014 The Korean Academy of Medical Sciences. http://creativecommons.org/licenses/by-nc/3.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Hwang, Joon Ho
Kim, Joo Heon
Hwang, Jung Ju
Kim, Kyu Soon
Kim, Seung Yeon
Pneumonectomy Case in a Newborn with Congenital Pulmonary Lymphangiectasia
title Pneumonectomy Case in a Newborn with Congenital Pulmonary Lymphangiectasia
title_full Pneumonectomy Case in a Newborn with Congenital Pulmonary Lymphangiectasia
title_fullStr Pneumonectomy Case in a Newborn with Congenital Pulmonary Lymphangiectasia
title_full_unstemmed Pneumonectomy Case in a Newborn with Congenital Pulmonary Lymphangiectasia
title_short Pneumonectomy Case in a Newborn with Congenital Pulmonary Lymphangiectasia
title_sort pneumonectomy case in a newborn with congenital pulmonary lymphangiectasia
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3991809/
https://www.ncbi.nlm.nih.gov/pubmed/24753713
http://dx.doi.org/10.3346/jkms.2014.29.4.609
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