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Idiopathic pulmonary hemosiderosis - a diagnostic challenge

Idiopathic pulmonary hemosiderosis is a rare disorder that can occur at any age and is characterized by the triad of hemoptysis, iron deficiency anemia and diffuse pulmonary infiltrates. The clinical course is exceedingly variable especially in children and a substantial proportion of this age group...

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Detalles Bibliográficos
Autores principales: Bakalli, Ilirjana, Kota, Luljeta, Sala, Durim, Celaj, Ermela, Kola, Elmira, Lluka, Robert, Sallabanda, Sashenka
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2014
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3999482/
https://www.ncbi.nlm.nih.gov/pubmed/24708654
http://dx.doi.org/10.1186/1824-7288-40-35
Descripción
Sumario:Idiopathic pulmonary hemosiderosis is a rare disorder that can occur at any age and is characterized by the triad of hemoptysis, iron deficiency anemia and diffuse pulmonary infiltrates. The clinical course is exceedingly variable especially in children and a substantial proportion of this age group is undiagnosed. It is probably due to the fact that iron deficiency anemia may be the first and the only manifestation of IPH, preceding other symptoms and signs by several months and IPH is not considered as a rare cause of anemia, unless the typical triad is present. We present a case of IPH in a 13-year-old girl, treated for several months with persistent iron deficiency anemia, without response to therapy.