Airway management of a child with frontometaphyseal dysplasia (Gorlin Cohen syndrome)

Frontometaphyseal dysplasia (FMD), also called Gorlin-Cohen syndrome, is a rare hereditary X-linked dominant craniotubular bone disorder. The presentation describes the airway management of a 2-year-old child suffering from FMD with significant retrognathia, posted for major long bone corrective ost...

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Detalles Bibliográficos
Autores principales: Ganigara, Anuradha, Nishtala, Madhavi, Chandrika, Yabagodu Rama Vakoda, Chandrakala, Kunigal Ravishankar
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2014
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4009657/
https://www.ncbi.nlm.nih.gov/pubmed/24803775
http://dx.doi.org/10.4103/0970-9185.130100
Descripción
Sumario:Frontometaphyseal dysplasia (FMD), also called Gorlin-Cohen syndrome, is a rare hereditary X-linked dominant craniotubular bone disorder. The presentation describes the airway management of a 2-year-old child suffering from FMD with significant retrognathia, posted for major long bone corrective osteotomy. Induction with a combination of dexmedetomidine and ketamine preceded a successful endotracheal intubation under spontaneous ventilation.

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