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Brain–blood amino acid correlates following protein restriction in murine maple syrup urine disease

BACKGROUND: Conventional therapy for patients with maple syrup urine disease (MSUD) entails restriction of protein intake to maintain acceptable levels of the branched chain amino acid, leucine (LEU), monitored in blood. However, no data exists on the correlation between brain and blood LEU with pro...

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Detalles Bibliográficos
Autores principales:	Vogel, Kara R, Arning, Erland, Wasek, Brandi L, McPherson, Sterling, Bottiglieri, Teodoro, Gibson, K Michael
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	BioMed Central 2014
Materias:	Research
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4022424/ https://www.ncbi.nlm.nih.gov/pubmed/24886632 http://dx.doi.org/10.1186/1750-1172-9-73

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