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Langerhans Cell Histiocytosis: An Illusion of Hope
Introduction: Langerhans cell histiocytosis (LCH) is a rare atypical cellular disorder characterized by clonal proliferation of Langerhans cells leading to myriad clinical presentations and variable outcomes. It usually occurs in children and young adults. It can be present with local and systemic m...
Autores principales: | , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
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Jaypee Brothers Medical Publishers
2013
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Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4034643/ https://www.ncbi.nlm.nih.gov/pubmed/25206193 http://dx.doi.org/10.5005/jp-journals-10005-1191 |
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author | Desai, Vela D Priyadarshinni, Smita R Varma, Beena Sharma, Rajeev |
author_facet | Desai, Vela D Priyadarshinni, Smita R Varma, Beena Sharma, Rajeev |
author_sort | Desai, Vela D |
collection | PubMed |
description | Introduction: Langerhans cell histiocytosis (LCH) is a rare atypical cellular disorder characterized by clonal proliferation of Langerhans cells leading to myriad clinical presentations and variable outcomes. It usually occurs in children and young adults. It can be present with local and systemic manifestation involving skin, bone, mucosal tissues and internal organs. Aims and objectives: The stomatologist plays an important role in management of the disease by keeping in mind the various oral manifestations of the disease. Case report: Of a child with disseminated LCH with multiorgan involvement who presented with failure to thrive, osteolytic bony lesions and extensive cutaneous eruptions. Conclusion: Early diagnosis and awareness is necessary to treat the patients. How to cite this article: Desai VD, Priyadarshinni SR, Varma B, Sharma R. Langerhans Cell Histiocytosis: An Illusion of Hope. Int J Clin Pediatr Dent 2013;6(1):66-70. |
format | Online Article Text |
id | pubmed-4034643 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2013 |
publisher | Jaypee Brothers Medical Publishers |
record_format | MEDLINE/PubMed |
spelling | pubmed-40346432014-09-09 Langerhans Cell Histiocytosis: An Illusion of Hope Desai, Vela D Priyadarshinni, Smita R Varma, Beena Sharma, Rajeev Int J Clin Pediatr Dent Case Report Introduction: Langerhans cell histiocytosis (LCH) is a rare atypical cellular disorder characterized by clonal proliferation of Langerhans cells leading to myriad clinical presentations and variable outcomes. It usually occurs in children and young adults. It can be present with local and systemic manifestation involving skin, bone, mucosal tissues and internal organs. Aims and objectives: The stomatologist plays an important role in management of the disease by keeping in mind the various oral manifestations of the disease. Case report: Of a child with disseminated LCH with multiorgan involvement who presented with failure to thrive, osteolytic bony lesions and extensive cutaneous eruptions. Conclusion: Early diagnosis and awareness is necessary to treat the patients. How to cite this article: Desai VD, Priyadarshinni SR, Varma B, Sharma R. Langerhans Cell Histiocytosis: An Illusion of Hope. Int J Clin Pediatr Dent 2013;6(1):66-70. Jaypee Brothers Medical Publishers 2013 2013-04-26 /pmc/articles/PMC4034643/ /pubmed/25206193 http://dx.doi.org/10.5005/jp-journals-10005-1191 Text en Copyright © 2013; Jaypee Brothers Medical Publishers (P) Ltd. This work is licensed under a Creative Commons Attribution 3.0 Unported License. To view a copy of this license, visit http://creativecommons.org/licenses/by/3.0/ |
spellingShingle | Case Report Desai, Vela D Priyadarshinni, Smita R Varma, Beena Sharma, Rajeev Langerhans Cell Histiocytosis: An Illusion of Hope |
title | Langerhans Cell Histiocytosis: An Illusion of Hope |
title_full | Langerhans Cell Histiocytosis: An Illusion of Hope |
title_fullStr | Langerhans Cell Histiocytosis: An Illusion of Hope |
title_full_unstemmed | Langerhans Cell Histiocytosis: An Illusion of Hope |
title_short | Langerhans Cell Histiocytosis: An Illusion of Hope |
title_sort | langerhans cell histiocytosis: an illusion of hope |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4034643/ https://www.ncbi.nlm.nih.gov/pubmed/25206193 http://dx.doi.org/10.5005/jp-journals-10005-1191 |
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