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Filamentous white matter prion protein deposition is a distinctive feature of multiple inherited prion diseases
BACKGROUND: Sporadic, inherited and acquired prion diseases show distinct histological patterns of abnormal prion protein (PrP) deposits. Many of the inherited prion diseases show striking histological patterns, which often associate with specific mutations. Most reports have focused on the pattern...
Autores principales: | Reiniger, Lilla, Mirabile, Ilaria, Lukic, Ana, Wadsworth, Jonathan DF, Linehan, Jacqueline M, Groves, Michael, Lowe, Jessica, Druyeh, Ronald, Rudge, Peter, Collinge, John, Mead, Simon, Brandner, Sebastian |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
BioMed Central
2013
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4046834/ https://www.ncbi.nlm.nih.gov/pubmed/24252267 http://dx.doi.org/10.1186/2051-5960-1-8 |
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