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Stilbenes and resveratrol metabolites improve mitochondrial fatty acid oxidation defects in human fibroblasts

BACKGROUND: Inborn enzyme defects of mitochondrial fatty acid beta-oxidation (FAO) form a large group of genetic disorders associated to variable clinical presentations ranging from life-threatening pediatric manifestations up to milder late onset phenotypes, including myopathy. Very few candidate d...

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Detalles Bibliográficos
Autores principales: Aires, Virginie, Delmas, Dominique, Le Bachelier, Carole, Latruffe, Norbert, Schlemmer, Dimitri, Benoist, Jean-François, Djouadi, Fatima, Bastin, Jean
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2014
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4051957/
https://www.ncbi.nlm.nih.gov/pubmed/24898617
http://dx.doi.org/10.1186/1750-1172-9-79

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