Huge Intrathoracic Malignant Peripheral Nerve Sheath Tumor in an Adolescent with Neurofibromatosis Type 1

Malignant peripheral nerve sheath tumor (MPNST) is a rare soft tissue malignancy usually found in patients with neurofibromatosis type 1 (NF1) with a poor outcome. Although MPNST can be found in any part of the body including head and neck or extremities, intrathoracic MPNST with or without NF1 is u...

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Detalles Bibliográficos
Autores principales: Yoon, Jong Hyung, Lee, Hyun-Sung, Chun, Jong In, Park, Seog-Yun, Park, Hyeon Jin, Park, Byung-Kiu
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi Publishing Corporation 2014
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4058178/
https://www.ncbi.nlm.nih.gov/pubmed/24971186
http://dx.doi.org/10.1155/2014/951252
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author Yoon, Jong Hyung
Lee, Hyun-Sung
Chun, Jong In
Park, Seog-Yun
Park, Hyeon Jin
Park, Byung-Kiu
author_facet Yoon, Jong Hyung
Lee, Hyun-Sung
Chun, Jong In
Park, Seog-Yun
Park, Hyeon Jin
Park, Byung-Kiu
author_sort Yoon, Jong Hyung
collection PubMed
description Malignant peripheral nerve sheath tumor (MPNST) is a rare soft tissue malignancy usually found in patients with neurofibromatosis type 1 (NF1) with a poor outcome. Although MPNST can be found in any part of the body including head and neck or extremities, intrathoracic MPNST with or without NF1 is uncommon, especially in children or adolescents. Reported herein is a case of huge intrathoracic MPNST in a 16-year-old girl with NF1, and a brief review of the literature.
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spelling pubmed-40581782014-06-26 Huge Intrathoracic Malignant Peripheral Nerve Sheath Tumor in an Adolescent with Neurofibromatosis Type 1 Yoon, Jong Hyung Lee, Hyun-Sung Chun, Jong In Park, Seog-Yun Park, Hyeon Jin Park, Byung-Kiu Case Rep Pediatr Case Report Malignant peripheral nerve sheath tumor (MPNST) is a rare soft tissue malignancy usually found in patients with neurofibromatosis type 1 (NF1) with a poor outcome. Although MPNST can be found in any part of the body including head and neck or extremities, intrathoracic MPNST with or without NF1 is uncommon, especially in children or adolescents. Reported herein is a case of huge intrathoracic MPNST in a 16-year-old girl with NF1, and a brief review of the literature. Hindawi Publishing Corporation 2014 2014-05-25 /pmc/articles/PMC4058178/ /pubmed/24971186 http://dx.doi.org/10.1155/2014/951252 Text en Copyright © 2014 Jong Hyung Yoon et al. https://creativecommons.org/licenses/by/3.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Yoon, Jong Hyung
Lee, Hyun-Sung
Chun, Jong In
Park, Seog-Yun
Park, Hyeon Jin
Park, Byung-Kiu
Huge Intrathoracic Malignant Peripheral Nerve Sheath Tumor in an Adolescent with Neurofibromatosis Type 1
title Huge Intrathoracic Malignant Peripheral Nerve Sheath Tumor in an Adolescent with Neurofibromatosis Type 1
title_full Huge Intrathoracic Malignant Peripheral Nerve Sheath Tumor in an Adolescent with Neurofibromatosis Type 1
title_fullStr Huge Intrathoracic Malignant Peripheral Nerve Sheath Tumor in an Adolescent with Neurofibromatosis Type 1
title_full_unstemmed Huge Intrathoracic Malignant Peripheral Nerve Sheath Tumor in an Adolescent with Neurofibromatosis Type 1
title_short Huge Intrathoracic Malignant Peripheral Nerve Sheath Tumor in an Adolescent with Neurofibromatosis Type 1
title_sort huge intrathoracic malignant peripheral nerve sheath tumor in an adolescent with neurofibromatosis type 1
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4058178/
https://www.ncbi.nlm.nih.gov/pubmed/24971186
http://dx.doi.org/10.1155/2014/951252
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