Combined Liver and Kidney Transplant in a Patient with Budd-Chiari Syndrome Secondary to Autosomal Dominant Polycystic Kidney Disease Associated with Polycystic Liver Disease: Report of a Case with a 9-Year Follow-Up

Polycystic liver disease (PLD) is a hereditary disease inherited by autosomal dominant trait that occurs as a frequent extrarenal manifestation of autosomal dominant polycystic kidney disease (ADPKD). We report a case of a 59-year-old woman diagnosed with ADPKD associated with PLD. End-stage chronic...

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Autores principales: Ramírez de la Piscina, Patricia, Duca, Ileana, Estrada, Silvia, Calderón, Rosario, Ganchegui, Idoia, Campos, Amaia, Spicakova, Katerina, Urtasun, Leire, Salvador, Marta, Delgado, Elvira, Bengoa, Raquel, García-Campos, Francisco
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi Publishing Corporation 2014
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4058590/
https://www.ncbi.nlm.nih.gov/pubmed/24987537
http://dx.doi.org/10.1155/2014/585291
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author Ramírez de la Piscina, Patricia
Duca, Ileana
Estrada, Silvia
Calderón, Rosario
Ganchegui, Idoia
Campos, Amaia
Spicakova, Katerina
Urtasun, Leire
Salvador, Marta
Delgado, Elvira
Bengoa, Raquel
García-Campos, Francisco
author_facet Ramírez de la Piscina, Patricia
Duca, Ileana
Estrada, Silvia
Calderón, Rosario
Ganchegui, Idoia
Campos, Amaia
Spicakova, Katerina
Urtasun, Leire
Salvador, Marta
Delgado, Elvira
Bengoa, Raquel
García-Campos, Francisco
author_sort Ramírez de la Piscina, Patricia
collection PubMed
description Polycystic liver disease (PLD) is a hereditary disease inherited by autosomal dominant trait that occurs as a frequent extrarenal manifestation of autosomal dominant polycystic kidney disease (ADPKD). We report a case of a 59-year-old woman diagnosed with ADPKD associated with PLD. End-stage chronic renal failure with a secondary Budd-Chiari syndrome developed during the patient's clinical course. She underwent combined liver and kidney transplantation, with a successful response over a 9-year follow-up period.
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spelling pubmed-40585902014-07-01 Combined Liver and Kidney Transplant in a Patient with Budd-Chiari Syndrome Secondary to Autosomal Dominant Polycystic Kidney Disease Associated with Polycystic Liver Disease: Report of a Case with a 9-Year Follow-Up Ramírez de la Piscina, Patricia Duca, Ileana Estrada, Silvia Calderón, Rosario Ganchegui, Idoia Campos, Amaia Spicakova, Katerina Urtasun, Leire Salvador, Marta Delgado, Elvira Bengoa, Raquel García-Campos, Francisco Case Rep Gastrointest Med Case Report Polycystic liver disease (PLD) is a hereditary disease inherited by autosomal dominant trait that occurs as a frequent extrarenal manifestation of autosomal dominant polycystic kidney disease (ADPKD). We report a case of a 59-year-old woman diagnosed with ADPKD associated with PLD. End-stage chronic renal failure with a secondary Budd-Chiari syndrome developed during the patient's clinical course. She underwent combined liver and kidney transplantation, with a successful response over a 9-year follow-up period. Hindawi Publishing Corporation 2014 2014-06-01 /pmc/articles/PMC4058590/ /pubmed/24987537 http://dx.doi.org/10.1155/2014/585291 Text en Copyright © 2014 Patricia Ramírez de la Piscina et al. https://creativecommons.org/licenses/by/3.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Ramírez de la Piscina, Patricia
Duca, Ileana
Estrada, Silvia
Calderón, Rosario
Ganchegui, Idoia
Campos, Amaia
Spicakova, Katerina
Urtasun, Leire
Salvador, Marta
Delgado, Elvira
Bengoa, Raquel
García-Campos, Francisco
Combined Liver and Kidney Transplant in a Patient with Budd-Chiari Syndrome Secondary to Autosomal Dominant Polycystic Kidney Disease Associated with Polycystic Liver Disease: Report of a Case with a 9-Year Follow-Up
title Combined Liver and Kidney Transplant in a Patient with Budd-Chiari Syndrome Secondary to Autosomal Dominant Polycystic Kidney Disease Associated with Polycystic Liver Disease: Report of a Case with a 9-Year Follow-Up
title_full Combined Liver and Kidney Transplant in a Patient with Budd-Chiari Syndrome Secondary to Autosomal Dominant Polycystic Kidney Disease Associated with Polycystic Liver Disease: Report of a Case with a 9-Year Follow-Up
title_fullStr Combined Liver and Kidney Transplant in a Patient with Budd-Chiari Syndrome Secondary to Autosomal Dominant Polycystic Kidney Disease Associated with Polycystic Liver Disease: Report of a Case with a 9-Year Follow-Up
title_full_unstemmed Combined Liver and Kidney Transplant in a Patient with Budd-Chiari Syndrome Secondary to Autosomal Dominant Polycystic Kidney Disease Associated with Polycystic Liver Disease: Report of a Case with a 9-Year Follow-Up
title_short Combined Liver and Kidney Transplant in a Patient with Budd-Chiari Syndrome Secondary to Autosomal Dominant Polycystic Kidney Disease Associated with Polycystic Liver Disease: Report of a Case with a 9-Year Follow-Up
title_sort combined liver and kidney transplant in a patient with budd-chiari syndrome secondary to autosomal dominant polycystic kidney disease associated with polycystic liver disease: report of a case with a 9-year follow-up
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4058590/
https://www.ncbi.nlm.nih.gov/pubmed/24987537
http://dx.doi.org/10.1155/2014/585291
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