Epstein-Barr virus induced hemophagocytic lymphohistiocytosis in X-linked lymphoproliferative disease

X-linked lymphoproliferative disease (XLP) is a rare, often fatal genetic disorder characterized by extreme vulnerability to Epstein-Barr virus (EBV). EBV-induced hemophagocytic lymphohistiocytosis (HLH) is a known presentation in XLP. In EBV-induced HLH in XLP, the brain imaging findings in the acu...

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Autores principales: Sankararaman, Senthilkumar, Riel-Romero, Rosario Maria, Jeroudi, Majed, Gonzalez-Toledo, Eduardo
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medknow Publications & Media Pvt Ltd 2014
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4064187/
https://www.ncbi.nlm.nih.gov/pubmed/24966560
http://dx.doi.org/10.4103/0976-3147.131669
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author Sankararaman, Senthilkumar
Riel-Romero, Rosario Maria
Jeroudi, Majed
Gonzalez-Toledo, Eduardo
author_facet Sankararaman, Senthilkumar
Riel-Romero, Rosario Maria
Jeroudi, Majed
Gonzalez-Toledo, Eduardo
author_sort Sankararaman, Senthilkumar
collection PubMed
description X-linked lymphoproliferative disease (XLP) is a rare, often fatal genetic disorder characterized by extreme vulnerability to Epstein-Barr virus (EBV). EBV-induced hemophagocytic lymphohistiocytosis (HLH) is a known presentation in XLP. In EBV-induced HLH in XLP, the brain imaging findings in the acute phase include a non specific pattern. In this report, we highlight the magnetic resonance imaging and magnetic resonance spectroscopy findings in a child with EBV induced HLH in XLP.
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spelling pubmed-40641872014-06-25 Epstein-Barr virus induced hemophagocytic lymphohistiocytosis in X-linked lymphoproliferative disease Sankararaman, Senthilkumar Riel-Romero, Rosario Maria Jeroudi, Majed Gonzalez-Toledo, Eduardo J Neurosci Rural Pract Case Report X-linked lymphoproliferative disease (XLP) is a rare, often fatal genetic disorder characterized by extreme vulnerability to Epstein-Barr virus (EBV). EBV-induced hemophagocytic lymphohistiocytosis (HLH) is a known presentation in XLP. In EBV-induced HLH in XLP, the brain imaging findings in the acute phase include a non specific pattern. In this report, we highlight the magnetic resonance imaging and magnetic resonance spectroscopy findings in a child with EBV induced HLH in XLP. Medknow Publications & Media Pvt Ltd 2014 /pmc/articles/PMC4064187/ /pubmed/24966560 http://dx.doi.org/10.4103/0976-3147.131669 Text en Copyright: © Journal of Neurosciences in Rural Practice http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Sankararaman, Senthilkumar
Riel-Romero, Rosario Maria
Jeroudi, Majed
Gonzalez-Toledo, Eduardo
Epstein-Barr virus induced hemophagocytic lymphohistiocytosis in X-linked lymphoproliferative disease
title Epstein-Barr virus induced hemophagocytic lymphohistiocytosis in X-linked lymphoproliferative disease
title_full Epstein-Barr virus induced hemophagocytic lymphohistiocytosis in X-linked lymphoproliferative disease
title_fullStr Epstein-Barr virus induced hemophagocytic lymphohistiocytosis in X-linked lymphoproliferative disease
title_full_unstemmed Epstein-Barr virus induced hemophagocytic lymphohistiocytosis in X-linked lymphoproliferative disease
title_short Epstein-Barr virus induced hemophagocytic lymphohistiocytosis in X-linked lymphoproliferative disease
title_sort epstein-barr virus induced hemophagocytic lymphohistiocytosis in x-linked lymphoproliferative disease
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4064187/
https://www.ncbi.nlm.nih.gov/pubmed/24966560
http://dx.doi.org/10.4103/0976-3147.131669
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