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Parry-Romberg syndrome with hemimasticatory spasm in pregnancy; A dystonia mimic
Parry-Romberg syndrome (PRS) with hemimasticatory spasm (HMS) is quite an uncommon overlapping phenomenon which very often mimics jaw closing dystonia. A previously healthy 35-year-old female, during her 5(th) month of pregnancy started developing intermittent unilateral painful spasms of jaw while...
Autores principales: | , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Medknow Publications & Media Pvt Ltd
2014
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4064192/ https://www.ncbi.nlm.nih.gov/pubmed/24966565 http://dx.doi.org/10.4103/0976-3147.131675 |
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author | Panda, Akhila Kumar Gopinath, Godhavarma Singh, Shaily |
author_facet | Panda, Akhila Kumar Gopinath, Godhavarma Singh, Shaily |
author_sort | Panda, Akhila Kumar |
collection | PubMed |
description | Parry-Romberg syndrome (PRS) with hemimasticatory spasm (HMS) is quite an uncommon overlapping phenomenon which very often mimics jaw closing dystonia. A previously healthy 35-year-old female, during her 5(th) month of pregnancy started developing intermittent unilateral painful spasms of jaw while conversation, clinching of teeth, or eating, which led to frequent tongue bites. The spasms were worsened during pregnancy. She used to do certain manoeuvre like sensory tricks in form of touching involved side of the face to relieve the symptoms. Apart from this, she developed progressive hemifacial and hemitongue atrophy. Other medical and neurological examinations were normal. Laboratory investigations as well as neuroimaging were noncontributory. The spasm responded to carbamazepine but hemifacial atrophy persists. To our best knowledge, onset and worsening of this syndrome in pregnancy has not been described earlier which might be correlated either with some hormonal imbalance or some unknown mechanisms. |
format | Online Article Text |
id | pubmed-4064192 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2014 |
publisher | Medknow Publications & Media Pvt Ltd |
record_format | MEDLINE/PubMed |
spelling | pubmed-40641922014-06-25 Parry-Romberg syndrome with hemimasticatory spasm in pregnancy; A dystonia mimic Panda, Akhila Kumar Gopinath, Godhavarma Singh, Shaily J Neurosci Rural Pract Case Report Parry-Romberg syndrome (PRS) with hemimasticatory spasm (HMS) is quite an uncommon overlapping phenomenon which very often mimics jaw closing dystonia. A previously healthy 35-year-old female, during her 5(th) month of pregnancy started developing intermittent unilateral painful spasms of jaw while conversation, clinching of teeth, or eating, which led to frequent tongue bites. The spasms were worsened during pregnancy. She used to do certain manoeuvre like sensory tricks in form of touching involved side of the face to relieve the symptoms. Apart from this, she developed progressive hemifacial and hemitongue atrophy. Other medical and neurological examinations were normal. Laboratory investigations as well as neuroimaging were noncontributory. The spasm responded to carbamazepine but hemifacial atrophy persists. To our best knowledge, onset and worsening of this syndrome in pregnancy has not been described earlier which might be correlated either with some hormonal imbalance or some unknown mechanisms. Medknow Publications & Media Pvt Ltd 2014 /pmc/articles/PMC4064192/ /pubmed/24966565 http://dx.doi.org/10.4103/0976-3147.131675 Text en Copyright: © Journal of Neurosciences in Rural Practice http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Panda, Akhila Kumar Gopinath, Godhavarma Singh, Shaily Parry-Romberg syndrome with hemimasticatory spasm in pregnancy; A dystonia mimic |
title | Parry-Romberg syndrome with hemimasticatory spasm in pregnancy; A dystonia mimic |
title_full | Parry-Romberg syndrome with hemimasticatory spasm in pregnancy; A dystonia mimic |
title_fullStr | Parry-Romberg syndrome with hemimasticatory spasm in pregnancy; A dystonia mimic |
title_full_unstemmed | Parry-Romberg syndrome with hemimasticatory spasm in pregnancy; A dystonia mimic |
title_short | Parry-Romberg syndrome with hemimasticatory spasm in pregnancy; A dystonia mimic |
title_sort | parry-romberg syndrome with hemimasticatory spasm in pregnancy; a dystonia mimic |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4064192/ https://www.ncbi.nlm.nih.gov/pubmed/24966565 http://dx.doi.org/10.4103/0976-3147.131675 |
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