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Oxidative brain damage in Mecp2-mutant murine models of Rett syndrome

Rett syndrome (RTT) is a rare neurodevelopmental disorder affecting almost exclusively females, caused in the overwhelming majority of the cases by loss-of-function mutations in the gene encoding methyl-CpG binding protein 2 (MECP2). High circulating levels of oxidative stress (OS) markers in patien...

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Detalles Bibliográficos
Autores principales:	De Felice, Claudio, Della Ragione, Floriana, Signorini, Cinzia, Leoncini, Silvia, Pecorelli, Alessandra, Ciccoli, Lucia, Scalabrì, Francesco, Marracino, Federico, Madonna, Michele, Belmonte, Giuseppe, Ricceri, Laura, De Filippis, Bianca, Laviola, Giovanni, Valacchi, Giuseppe, Durand, Thierry, Galano, Jean-Marie, Oger, Camille, Guy, Alexandre, Bultel-Poncé, Valérie, Guy, Jacky, Filosa, Stefania, Hayek, Joussef, D'Esposito, Maurizio
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Academic Press 2014
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4076513/ https://www.ncbi.nlm.nih.gov/pubmed/24769161 http://dx.doi.org/10.1016/j.nbd.2014.04.006

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